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1.
Cir. Urug ; 6(1): e306, jul. 2022. ^eilus
Artigo em Espanhol | LILACS, UY-BNMED, BNUY | ID: biblio-1404120

RESUMO

El condrosarcoma forma parte de los tumores primarios malignos más frecuentes. Las localizaciones pélvicas y de raíz de muslo requerirán abordajes amplios con la consecuente dificultad de cobertura de partes blandas. La hemipelvectomía externa es habitualmente el procedimiento de elección para estas localizaciones. Implica la resección de la extremidad inferior en bloque asociada a la hemipelvis ipsilateral, dando como resultado un gran defecto de cobertura. En algunas circunstancias, la extensa resección de partes blandas hace imposible la utilización de colgajos rotacionales locales. La reconstrucción con colgajo tipo "Fillet flaps" ofrece a estos defectos de partes blandas la opción de lograr una adecuada cobertura. El objetivo del trabajo es mostrar la resolución de un caso poco convencional de condrosarcoma de fémur proximal y su reconstrucción de partes blandas con un método nunca antes utilizado en nuestro medio.


Chondrosarcoma is one of the most frequent malignant primary tumors. Pelvic and proximal femur locations require extensive approaches with the consequent difficulty of soft tissue reconstruction. External hemipelvectomy is usually the procedure for these locations. It involves total en bloc resection of the lower extremity associated with ipsilateral hemipelvis, resulting in a large coverage defect. In some cases, local rotational flaps are impossible. Reconstruction with fillet flaps offers an adequate coverage for soft tissue defects. The objective of this study is to show the resolution of an unconventional case of chondrosarcoma of the proximal femur and its soft tissue reconstruction with a method never before used in our country.


O condrossarcoma é um dos tumores primários malignos mais frequentes. As localizações das raízes pélvicas e da coxa exigirão amplas abordagens com a conseqüente dificuldade em cobrir os tecidos moles. A hemipelvectomia externa costuma ser o procedimento de escolha para esses locais. Envolve a ressecção do membro inferior em bloco associado à hemipelve ipsilateral, resultando em um grande defeito de cobertura. Em algumas circunstâncias, a ressecção extensa de partes moles impossibilita o uso de retalhos rotacionais locais. A reconstrução com retalhos de filé oferece a esses defeitos de tecidos moles a opção de obter uma cobertura adequada. O objetivo deste trabalho é mostrar a resolução de um caso não convencional de condrossarcoma do fêmur proximal e sua reconstrução de partes moles com método nunca antes utilizado em nosso meio.


Assuntos
Humanos , Masculino , Adulto , Retalhos Cirúrgicos/transplante , Condrossarcoma/cirurgia , Procedimentos de Cirurgia Plástica/métodos , Neoplasias Femorais/cirurgia , Hemipelvectomia/métodos , Condrossarcoma/diagnóstico por imagem , Neoplasias Femorais/diagnóstico por imagem
2.
Gac. méd. boliv ; 44(1): 99-102, jun. 2021. ilus
Artigo em Espanhol | LILACS | ID: biblio-1286581

RESUMO

El siguiente caso, se trata de una paciente de sexo femenino que acude a consulta de traumatología por dolor de rodilla y dificultad para deambular, sin antecedente de trauma. En la radiografía anteroposterior y lateral se evidencia múltiples áreas radiolúcidas y escleróticas en meseta tibial y fémur distal derecho. La biopsia reporta: Condrosarcoma indiferenciado Grado 2. Se inicia sesiones de quimioterapia profiláctica y se planifica la cirugía de salvamento, esto ante la negativa de la paciente para aceptar la cirugía de amputación. La cirugía de reconstrucción se realizó mediante la colocación de una prótesis semiconstreñida tipo Endo Model cementada. En el posoperatorio se realizó controles y curaciones semanales, con buena cicatrización de la herida, y posteriormente rehabilitación por fisioterapia. Actualmente la paciente puede deambular con apoyo y casi de manera independiente.


The following case is a female patient who came to the trauma clinic for knee pain and difficulty walking, with no history of trauma.The anteroposterior and lateral radiograph shows multiple radiolucent and sclerotic areas on the tibial plateau and the right distal femur.The biopsy reports grade 2 undifferentiated chondrosarcoma. Prophylactic chemotherapy sessions are started and salvage surgery is planned, this given the patient's refusal to accept amputation surgery. Reconstruction surgery was performed by placing a semi-constrained, cemented endo Model type prosthesis. In the postoperative period, weekly controls and dressings were carried out, with good wound healing and later rehabilitation by physiotherapy. Actually the patient can walk with support and almost independently.


Assuntos
Condrossarcoma
3.
Clinics ; 76: e2914, 2021. tab, graf
Artigo em Inglês | LILACS | ID: biblio-1350607

RESUMO

OBJECTIVES: The aim of this study was to evaluate the role of amphiregulin protein, an epidermal growth factor receptor ligand, in cartilaginous tumors. METHODS: Amphiregulin expression was examined in 31 enchondromas and 67 chondrosarcomas using immunohistochemistry analysis. RESULTS: Overall, 15 enchondromas (48.40%) and 24 chondrosarcomas (35.82%) were positive for amphiregulin. According to the receiver operating characteristic curve test, no difference in amphiregulin expression was observed between enchondromas and low-grade chondrosarcomas (p=0.0880). Additionally, 39 lesions (16 in short bones, 13 in long bones, and 10 in flat bones) were positive for amphiregulin, exhibiting a higher percentage of positive cells (p=0.0030) and intensity of immunohistochemical expression (p=0.0055) in short bone lesions than in others. Among 25 enchondromas localized in short bones, 15 expressed amphiregulin; however, all 6 cases localized in long bones were negative for this marker (p=0.0177). CONCLUSIONS: Amphiregulin did not help in distinguishing enchondromas from low-grade chondrosarcomas. The present study is the first to document the expression of this immunohistochemical marker in enchondromas. Furthermore, amphiregulin expression in enchondromas was localized in short bones, indicating a phenotypic distinction from that in long bones. This distinction may contribute to an improved understanding of the pathogenesis of these lesions.


Assuntos
Humanos , Neoplasias Ósseas , Condroma , Condrossarcoma , Anfirregulina/genética , Imuno-Histoquímica
4.
Clin. biomed. res ; 41(2): 190-191, 2021.
Artigo em Inglês | LILACS | ID: biblio-1341980

RESUMO

Chondrosarcoma is the third most common primary bone malignancy, but its thoracic presentation is unusual compared to the pelvis and extremities. Chest wall chondrosarcomas are difficult to be surgically resected due to their proximity to neurovascular structures. We report the case of a 48-year-old man presenting with a history of chest bulging. Computed tomography showed a lesion of approximately 12 cm in the sagittal axis adjacent to the upper lobe of the left lung, compressing the upper lobar bronchus and causing parenchymal atelectasis. Biopsy revealed chondrosarcoma. The lesion extrinsically compressed the left pectoralis major muscle and invaded the left pectoralis minor muscle. After complete surgical resection, the patient was discharged on postoperative day 20. (AU)


Assuntos
Humanos , Masculino , Pessoa de Meia-Idade , Condrossarcoma/diagnóstico , Condrossarcoma/cirurgia
5.
Autops. Case Rep ; 11: e2021322, 2021. graf
Artigo em Inglês | LILACS | ID: biblio-1285391

RESUMO

Only 14 cases of extraskeletal myxoid chondrosarcoma (EMC) of the vulva have been documented in the literature. We report a case of a 63-year-old woman with EMC of the vulva confirmed by both EWSR1 and NR4A3 fluorescence in situ hybridization, the latter of which is a more specific probe for this entity. The unusual location of this tumor of prominent myxoid morphology gave rise to a wide differential diagnosis, which necessitated thorough histologic evaluation and confirmatory ancillary testing in the form of immunohistochemistry and cytogenetic studies. This article aims to review extraskeletal myxoid chondrosarcoma of the vulva and various diagnostic clues to help differentiate it from its histologic mimics. This is the fifth case of vulvar EMC in the literature with confirmation of a NR4A3 gene rearrangement.


Assuntos
Humanos , Feminino , Pessoa de Meia-Idade , Neoplasias de Tecidos Moles , Vulva/anormalidades , Condrossarcoma/patologia , Proteína EWS de Ligação a RNA , Diagnóstico Diferencial , Membro 3 do Grupo A da Subfamília 4 de Receptores Nucleares
7.
Rev. argent. neurocir ; 34(3): 216-222, sept. 2020. ilus
Artigo em Espanhol | LILACS, BINACIS | ID: biblio-1120948

RESUMO

El condrosarcoma ocupa el tercer puesto dentro de las neoplasias óseas primarias, siendo la columna vertebral una localización inusual. Según su etiología se clasifican en condrosarcoma primario o secundario a lesiones subyacentes de tipo cartilaginosa como el encondroma u osteocondroma; siendo entre el 80-90% de bajo grado. Pueden presentarse en cualquier nivel de la columna vertebral, siendo más frecuente en la región torácica y cervical, comprometiendo los elementos posteriores de la vértebra, los cuerpos vertebrales o ambos, en un 40%, 15% y 45% respectivamente. El síntoma más común es el dolor localizado asociado a manifestaciones neurológicas. El método diagnóstico de elección es la biopsia por punción y el tratamiento se basa fundamentalmente en la resección quirúrgica


Chondrosarcoma occupies the third position within the primary bony neoplasia's, with an unusual location at the level of the spine. According to their etiology, they are classified as primary chondrosarcoma or secondary to underlying cartilaginous lesions such as the enchondroma or osteochondroma, being between 80-90% of low grade. They can occur at any level of the spine, being more frequent in the thoracic and cervical region, compromising the posterior elements of the vertebra, the vertebral body or both, by 40%, 15% and 45% respectively. The most common symptom is localized pain associated with neurological manifestations. The diagnostic method of choice is biopsy and treatment is based primarily on surgical resection.


Assuntos
Humanos , Condrossarcoma , Coluna Vertebral , Neoplasias Ósseas , Osteocondroma , Condroma
8.
Arch. argent. pediatr ; 118(1): e34-e38, 2020-02-00. ilus
Artigo em Espanhol | LILACS, BINACIS | ID: biblio-1095860

RESUMO

La osteocondromatosis sinovial es una metaplasia benigna de la membrana sinovial que afecta a 1 de cada 100 000 personas, en su mayoría adultos, y es extremadamente infrecuente en edad pediátrica. Predomina en grandes articulaciones, sobre todo la rodilla, y la sintomatología es, por lo general, inespecífica. Dado que la radiografía simple no suele ser concluyente, se recurre a la resonancia magnética nuclear y a la tomografía axial computarizada para orientar el diagnóstico. Se expone el caso de una paciente de 10 años de edad con gonalgia y dismorfia en la patela izquierda de seis meses de evolución, con diagnóstico de osteocondromatosis sinovial. Se presenta el caso dado que se trata de una entidad muy rara en niños, pero que requiere un tratamiento quirúrgico precoz para evitar sus posibles complicaciones, como la destrucción articular progresiva o la malignización a condrosarcoma.


Synovial osteochondromatosis consists of a synovial metaplasia which affects 1 per 100 000 people. It is a very rare disease among children. It typically affects large joints of the body, especially the knee. Due to the lack of specificity of the signs and symptoms and X-Ray images, imaging tests such as nuclear magnetic resonance or computerized tomography are frequently needed for diagnosis.We report a case of a ten-year-old female patient with a six months history of pain and deformity of left patella which was diagnosed with synovial osteochondromatosis. This case highlights the importance of clinical suspicion, not only because it is an extremely rare disease in children, but also because it needs a surgical treatment as soon as possible in order to avoid consequences it might have in pediatric age, as joint destruction or malignization to chondrosarcoma.


Assuntos
Humanos , Feminino , Criança , Condromatose Sinovial/cirurgia , Condromatose Sinovial/diagnóstico por imagem , Condromatose Sinovial/terapia , Condrossarcoma/prevenção & controle , Articulação do Joelho/anormalidades , Metaplasia
9.
Autops. Case Rep ; 10(3): e2020166, 2020. graf
Artigo em Inglês | LILACS | ID: biblio-1131826

RESUMO

The chest wall chondrosarcoma (CWC) is a rare slowly growing primary tumor of the chest wall with an incidence of <0.5 per million person-years. We present the case of a giant CWC that caused a mass effect on the mediastinum, heart, and lung. Large tumors with thoracic structures compression may be life threatening, and its resection and subsequent chest wall reconstruction represent a significant multidisciplinary surgical challenge. In this case, despite the large tumor dimensions, the preoperative planning—sparing key reconstructive options without compromising the tumor resection—allowed a complete en bloc tumor excision of a grade III chondrosarcoma with negative histologic margins. Successful reconstruction of the large full-thickness chest wall defect, with a latissimus dorsi muscle flap and methyl methacrylate incorporated into a polypropylene mesh in a sandwich fashion, was accomplished. Patient recovery was uneventful with good functional and aesthetic outcomes, and no evidence of recurrence at 1.5 years follow-up. This case report illustrates the main clinical, radiological, and histologic features of a CWC while discussing the surgical goals and highlighting the principles for chest wall reconstruction following extensive resection of a large and rare entity.


Assuntos
Humanos , Masculino , Pessoa de Meia-Idade , Neoplasias Ósseas/cirurgia , Condrossarcoma/cirurgia , Procedimentos de Cirurgia Plástica , Parede Torácica/patologia , Coração , Pulmão , Mediastino
10.
Rev. cuba. cir ; 58(4): e700, oct.-dic. 2019. graf
Artigo em Espanhol | LILACS, CUMED | ID: biblio-1126397

RESUMO

RESUMEN El condrosarcoma es definido como un tumor maligno con diferenciación de cartílago hialino puro que puede presentar cambios mixoides, calcificación y osificación. El objetivo es mostrar el resultado del tratamiento de una diseminación peritoneal a partir de un condrosarcoma costal. Se realizó una revisión de la literatura, las indicaciones y técnicas en el tratamiento de la diseminación peritoneal del condrosarcoma y se presentan los resultados en una paciente diagnosticada e intervenida en el Hospital Clínico Quirúrgico "Hermanos Ameijeiras", entre enero de 2014 y diciembre de 2017. Paciente femenina de 46 años, que 7 años antes presentó un aumento de volumen en región costal baja izquierda y fue intervenida quirúrgicamente. Con el diagnóstico de condrosarcoma, se realizó una resección costal en la primera ocasión y luego, en dos oportunidades más por recidiva tumoral, en la última intervención se coloca una prótesis de polipropileno. Dos años después de la última cirugía, acude de nuevo con un aumento de volumen en la parte baja (región tóraco-abdominal, línea axilar), salvo este síntoma, exhibía un estado general excelente. La diseminación peritoneal del condrosarcoma es excepcional, muy poco reportado a nivel mundial y con pocas experiencias en su tratamiento. Se realizó técnica de resección multivisceral y peritonectomía con quimioterapia adyuvante posoperatoria. No hubo complicaciones relacionadas con el proceder y se realizó una segunda intervención extensa por recidiva a los 2 años(AU)


ABSTRACT Chondrosarcoma is defined as a malignant tumor with pure hyaline cartilage differentiation and that may be accompanied with myxoid changes, calcification, and ossification. The objective is to show the treatment outcome for peritoneal dissemination from a rib chondrosarcoma. A review of the literature was carried out, as well as the indications and techniques corresponding to the treatment of chondrosarcoma peritoneal dissemination. The outcomes are presented in a patient diagnosed and operated on at Hermanos Ameijeiras Clinical-Surgical Hospital, between January 2014 and December 2017. Female patient, 46 years old, who, seven years earlier, had presented increased volume in the left lower rib region and undergone surgery. With the diagnosis of chondrosarcoma, a rib resection was performed the first time, and then, on two more occasions due to tumor recurrence, a polypropylene prosthesis was placed in the last intervention. Two years after the last surgery, she returned with increased volume in the lower part (thoracoabdominal region, axillary line), except for the following symptom: she exhibited an excellent general condition. Theperitoneal dissemination of chondrosarcoma is exceptional, very little reported worldwide, and with little treatment experience. A multivisceral resection and peritonectomy technique was performed with postoperative adjuvant chemotherapy. There were no complications related to the procedure and a second extensive intervention was performed after two-year relapse(AU)


Assuntos
Humanos , Feminino , Pessoa de Meia-Idade , Neoplasias Ósseas/tratamento farmacológico , Condrossarcoma/cirurgia , Condrossarcoma/diagnóstico , Literatura de Revisão como Assunto , Quimioterapia Adjuvante/métodos
11.
Acta ortop. mex ; 33(5): 325-328, sep.-oct. 2019. tab, graf
Artigo em Espanhol | LILACS | ID: biblio-1284965

RESUMO

Resumen: El síndrome de Maffucci se caracteriza por la presencia de múltiples encondromas y hemangiomas que pueden afectar tejidos blandos y otros órganos. El riesgo de transformación maligna de las lesiones es de 100% durante la vida del individuo, siendo el condrosarcoma el tumor maligno más frecuentemente asociado. Se presenta el caso de un hombre de 44 años de edad con diagnóstico de síndrome de Maffucci, el cual desarrolló un doble primario sincrónico: condrosarcoma y sarcoma fusocelular de alto grado multicéntrico de región escapular y tricipital, fue tratado con desarticulación interescapulotorácica, mostró progresión acelerada y enfermedad pulmonar. Existen otras neoplasias asociadas al síndrome de Maffucci tales como adenocarcinoma de páncreas, tumores mesenquimales de ovario, gliomas, astrocitomas y tumores de la pituitaria. Por lo que resulta muy interesante reportar la asociación infrecuente entre un sarcoma fusocelular y un condrosarcoma secundario en pacientes con síndrome de Maffucci. El seguimiento en este grupo de pacientes es complejo y se basa en la búsqueda intencionada de lesiones con crecimiento acelerado, prestando atención en lesiones de crecimiento progresivo, síntomas clínicos o datos radiológicos de malignidad.


Abstract: Maffucci syndrome is characterized by the presence of multiple enchondromes and hemangiomas that can affect soft tissues and other organs. The risk of malignant transformation of lesions is 100% during the life of the individual, with chondrosarcoma being the most frequently associated malignant tumor. We present the case of a 44-year-old man diagnosed with Maffucci syndrome who developed a synchronous double primary: chondrosarcoma and high-grade multicenter fusocellular sarcoma of scapular and tricipital region, was treated with disarticulation interscapule-thoracic, presented accelerated progression and lung disease. There are other neoplasms associated with Maffucci syndrome, such as pancreatic adenocarcinoma, mesenchymal ovarian tumors, gliomas, astrocytomas and pituitary tumors. It is therefore very interesting to report the uncommon association between fusocellular sarcoma and secondary chondrosarcoma in patients with Maffucci syndrome. Follow-up in this group of patients is complex and is based on the intentional search for accelerated growing lesions, paying attention to progressive growth injuries, clinical symptoms or radiological malignancy data.


Assuntos
Humanos , Adulto , Neoplasias Ósseas/cirurgia , Neoplasias Ósseas/complicações , Adenocarcinoma/cirurgia , Adenocarcinoma/complicações , Condrossarcoma/cirurgia , Condrossarcoma/complicações , Encondromatose/cirurgia , Encondromatose/complicações
12.
Acta ortop. mex ; 32(2): 108-111, mar.-abr. 2018. graf
Artigo em Espanhol | LILACS | ID: biblio-1019340

RESUMO

Resumen: Se presentan dos casos de una familia con diagnóstico de osteocondromatosis múltiple, el cual fue confirmado por estudio molecular con mutación sin sentido en heterocigosis c.1219C>T, (p.Gln407Stop) en el gen EXT1. En el primer caso, en un paciente se presentó deformidad de Madelung como hallazgo infrecuente y en el otro caso, condrosarcoma como complicación temida, resaltando la variación intrafamiliar, por lo que se recomienda la evaluación individual e interdisciplinaria. Además, ante una entidad genética debe brindarse el adecuado y oportuno asesoramiento genético familiar a todos sus integrantes.


Abstract: We present two cases of a family with the diagnosis of multiple osteochondromatosis, which was confirmed by molecular study with nonsense in heterozygosis mutation c.1219C>T, (p.Gln407Stop) in the EXT1 gene. In these cases, the Madelung deformity was presented in one patient as an uncommon finding and chondrosarcoma as a feared complication in the other case, highlighting intrafamilial variation, which is why individual and interdisciplinary evaluation is recommended. In addition, before a genetic entity should provide adequate and timely family genetic counseling to all its members.


Assuntos
Humanos , Neoplasias Ósseas/genética , Exostose Múltipla Hereditária/genética , Condrossarcoma/genética , N-Acetilglucosaminiltransferases/genética , Mutação
13.
Rev. bras. ortop ; 52(6): 748-754, Nov.-Dec. 2017. graf
Artigo em Inglês | LILACS | ID: biblio-899206

RESUMO

ABSTRACT Chondrosarcoma is a malignant cartilage-forming neoplasm. It is difficult to treat because of resistance to both chemotherapy and radiation, making wide local excision the only treatment. This report presents an active, 43 year-old man who was diagnosed with recurrent clear cell chondrosarcoma of the proximal left femur, previously reconstructed with a total hip prosthesis, extending to the weight-bearing dome of the acetabulum. Cancer staging study revealed no signs of tumor dissemination at distance. Given the excellent functional status of the patient, the authors performed a Enneking-Dunham type periacetabular pelvic resection and resected en bloc, with the total hip prosthesis including 22 cm of the femur and a portion of the hip abductor apparatus. Acetabular reconstruction was performed with a non-cemented pedestal cup prosthesis fixed at the iliac, and in-femur reconstruction utilized a cemented silver-coated proximal femur modular prosthesis. Today, after a 10-year follow-up, the patient is walking without crutches, he practices recreational cycling without assistance, and he is asymptomatic and free of tumoral disease. At present, no signs of relevant loosening, instability, infection, heterotopic ossification, or any other complications have been observed. Pelvic reconstructions are challenging and risky surgeries; however, the appearance of more functional implants, like the pedestal cup prosthesis, and its correct application and indication, may allow promising clinical and functional results with low complications rate.


RESUMO O condrossarcoma é uma neoplasia maligna formadora de cartilagem. O tratamento é difícil, devido à resistência tanto à quimioterapia como à radiação; a excisão local ampla é o único tratamento. O presente estudo relata o caso de um homem ativo de 43 anos diagnosticado com condrossarcoma de células claras do fêmur esquerdo proximal recorrente, previamente reconstruído com prótese total de quadril, estendia-se à abóbada do acetábulo, que sustenta peso. O estudo de estadiamento de câncer não revelou sinais de disseminação tumoral a distância. Considerando o excelente estado funcional do paciente, os autores fizeram uma ressecção pélvica periacetabular do tipo Enneking-Dunham com ressecção em bloco, com a prótese total do quadril, incluiu 22 cm do fêmur e uma porção do aparelho abdutor do quadril. A reconstrução acetabular foi feita com uma prótese de pedestal não cimentada fixada no ilíaco e a reconstrução no fêmur usou uma prótese modular cimentada para o fêmur proximal com revestimento em prata. Hoje, após um seguimento de dez anos, o paciente anda sem muletas, pratica ciclismo recreativo sem assistência e está assintomático e livre de doença tumoral. Não foram observados sinais de afrouxamento relevante, instabilidade, infecção, ossificação heterotópica ou quaisquer outras complicações. As reconstruções pélvicas são cirurgias difíceis e arriscadas; entretanto, o surgimento de implantes mais funcionais, como a prótese de pedestal, e sua correta aplicação e indicação podem permitir resultados clínicos e funcionais promissores, com baixa taxa de complicações.


Assuntos
Humanos , Masculino , Adulto , Neoplasias Ósseas , Condrossarcoma , Pelve
15.
Rev. Asoc. Argent. Ortop. Traumatol ; 82(2): 109-115, jun. 2017. []
Artigo em Espanhol | LILACS, BINACIS | ID: biblio-896258

RESUMO

Introducción: Los tumores del sacro representan <7% de los tumores espinales, prevalecen los tumores secundarios por mieloma múltiple o carcinomas de próstata, mama, pulmón o colón. El cordoma es el tumor maligno primario más frecuente y el tumor de células gigantes es la lesión benigna más común. Por su evolución, compromiso de estructuras extraóseas y la escasa respuesta a los tratamientos coadyuvantes, la cirugía es el tratamiento más utilizado, la vía de abordaje y la necesidad de instrumentación dependerán del tumor por tratar. Los objetivos de este trabajo son: evaluar el uso de la resección parcial del sacro, analizar la técnica quirúrgica y reconocer las complicaciones. Materiales y Métodos: Cuatro pacientes con diagnóstico de tumor sacro ubicado por debajo de S1, que consultan por dolor y cuyas imágenes confirman la lesión. A todos se les realiza una resección en bloque por vía posterior preservando S1. Se describe la técnica. Resultados: Los estudios anatomopatológicos revelaron: un cordoma, un tumor maligno de vaina nerviosa, un condrosarcoma y una metástasis de carcinoma prostático. Se preservó la función de S1 en todos los pacientes; uno tiene disfunción vesical permanente. Se observaron una dehiscencia de la herida, una infección y una fístula de líquido cefalorraquídeo. Todos permanecen sin la enfermedad tras un seguimiento de entre 6 y 24 meses. Conclusiones: La resección parcial del sacro por abordaje posterior único se puede indicar cuando la lesión compromete desde S2 hacia distal y no hay compromiso sacroilíaco. La preservación de raíces es de vital importancia para garantizar mejores resultados posoperatorios y una menor tasa de infección. Nivel de Evidencia: IV


Introduction: Tumors of the sacrum represent less than 7% of spinal tumors. Secondary tumors due to multiple myeloma or prostate, breast, lung and colon carcinomas predominate. Chordoma is the most frequent primary malignant tumor and giant cell tumor is the most common benign lesion. For its evolution, involvement of extra bone structures and poor response to the adyuvant therapy, surgery is the most commonly used treatment, the approach and the need for instrumentation depend on tumor to treat. The objectives of this study are to evaluate the use of partial resection of sacrum, analyze the surgical technique and assess complications. Methods: Four patients with diagnosis of sacral tumor below S1, who presented with pain and images confirming the injury. All underwent an en bloc resection by posterior via preserving S1. The technique is described. Results: The pathological results were: a chordoma, a malignant nerve sheath tumor, a chondrosarcoma and a metastasis of prostatic carcinoma. S1 function was preserved in all patients; one has permanent bladder dysfunction. Wound dehiscence, infection and cerebrospinal fluid fistula were detected. Patients are free of disease after a follow-up of 6-24 months. Conclusions: Partial resection of the sacrum using a unique posterior approach may be indicated when the injury involves from S2 distally and no sacroiliac involvement is observed. Root preservation is vital to guarantee the best postoperative results and a lower rate of infection. Level of Evidence: IV


Assuntos
Pessoa de Meia-Idade , Sacro/cirurgia , Neoplasias da Coluna Vertebral/cirurgia , Cordoma/cirurgia , Condrossarcoma/cirurgia , Procedimentos de Cirurgia Plástica , Seguimentos , Resultado do Tratamento
16.
Rev. otorrinolaringol. cir. cabeza cuello ; 77(2): 175-180, jun. 2017. ilus
Artigo em Espanhol | LILACS | ID: biblio-902759

RESUMO

El cáncer de laringe es un tumor relativamente raro en Ecuador (0,5/100000 varones). Las lesiones neoplásicas de laringe son usualmente epiteliales y el tipo histológico más frecuente es el carcinoma escamocelular. El tumor mesenquimal más común es el condrosarcoma. En los 31 años de existencia del Registro Nacional de Tumores de Ecuador éste es el primer caso de condrosarcoma de laringe registrado. Por este motivo, hemos decidido reportar el manejo diagnóstico y terapéutico de este caso.


Laryngeal cancer is a relatively uncommon tumor en Ecuador (0,5/100000 males). These neoplastic lesions usually epithelial and the most frequent histological type is squamous cell carcinoma. The most common mesenchymal tumor is chondrosarcoma. No case of this type of laryngeal tumor has been registered since the foundation of the National Cancer Registry of Ecuador thirty-one years ago. For this reason, we have decided to report the diagnostic and therapeutic management of his case.


Assuntos
Humanos , Masculino , Idoso , Neoplasias Laríngeas/cirurgia , Condrossarcoma/cirurgia , Laringectomia/métodos , Tireoidectomia , Tomografia Computadorizada por Raios X , Neoplasias Laríngeas/diagnóstico , Condrossarcoma/diagnóstico
17.
Rev. AMRIGS ; 61(1): 40-44, jan.-mar. 2017. tab
Artigo em Português | LILACS | ID: biblio-849163

RESUMO

Introdução: Condrossarcomas correspondem a 18% das tumorações ósseas malignas e podem apresentar comportamento agressivo, além de um mau prognóstico. Uma avaliação atualizada quanto às suas características e uma revisão da literatura que aborda o assunto são de grande valia. Este trabalho visa demonstrar o padrão epidemiológico e fisiopatológico dos casos de condrossarcoma envolvidos. Métodos: Foram incluídos 32 pacientes diagnosticados e acompanhados no Hospital São Lucas da PUCRS entre 2004 e 2015 e que tiveram seus prontuários revisados. Resultados: Com discreta prevalência entre as mulheres (59,3% dos casos), obteve-se média etária geral de 53,5 anos de idade. Uma fração de 37,5% dos pacientes apresentou metástases, cujo local de acometimento principal foi o pulmão. Quanto ao sítio primário, Ilíaco e ossos longos foram os mais envolvidos. Em comparação com estudos epidemiológicos realizados em outros países, os resultados aqui presentes obtiveram sincronia em alguns quesitos, como idade, local de manifestação primária ou do sítio de metástase. Já quanto ao gênero dos pacientes envolvidos e às características histológicas, algumas divergências foram detectadas. Conclusões: Ao avaliar condrossarcomas, o perfil populacional da região avaliada deve ser levado em consideração, gerando variações nos levantamentos epidemiológicos obtidos (AU)


Introduction: Chondrosarcomas correspond to 18% of malignant bone tumors and may present aggressive behavior in addition to a poor prognosis. An up-to-date assessment of their characteristics and a review of the literature that deals with the subject are valuable. This work aims to demonstrate the epidemiological and pathophysiological pattern of the cases of chondrosarcoma involved. Methods: Thirty-two patients diagnosed and followed up at the São Lucas Hospital of PUCRS between 2004 and 2015 were included and their records were reviewed. Results: With a slight prevalence among women (59.3% of the cases), the mean age was 53.5 years old. A fraction of 37.5% of the patients had metastases, whose main site affected was the lung. As for the primary site, the iliac and long bones were the most involved. Compared with epidemiological studies conducted in other countries, the results reported here were synchronized in some aspects, such as age, place of primary manifestation or site of metastasis. However, regarding the gender of the patients involved and the histological characteristics, some divergences were detected. Conclusions: When assessing chondrosarcomas, the population profile of the evaluated region should be taken into account, generating variations in the epidemiological surveys obtained (AU)


Assuntos
Humanos , Masculino , Feminino , Adulto , Pessoa de Meia-Idade , Idoso , Neoplasias Ósseas/epidemiologia , Condrossarcoma/epidemiologia , Fatores Etários , Brasil/epidemiologia , Condrossarcoma/terapia , Gradação de Tumores , Metástase Neoplásica
18.
ARS med. (Santiago, En línea) ; 42(3): 23-25, 2017. ilus
Artigo em Espanhol | LILACS | ID: biblio-1017236

RESUMO

El condrosarcoma espinal es un tumor maligno primario de la columna vertebral poco prevalente, ubicándose en mayor frecuencia a nivel torácico y lumbosacro. La dorsalgia de predominio nocturno es el principal síntoma y los signos de mielopatía por compresión los menos frecuentes. El diagnóstico requiere de estudios imagenológicos como la tomografía computarizada (TC) y resonancia magnética (RM). El tratamiento es quirúrgico y según su histopatología definirá la terapia coadyuvante. Presentamos un paciente con dorsalgia crónica y hemiparesia izquierda; donde la RM evidenció una lesión tumoral a nivel de T1-T3, realizándose resección quirúrgica con posterior reporte histopatológico de condrosarcoma grado II.(AU)


Spinal chondrosarcoma is a primary malignant tumor of the spine that is not very prevalent, being located more frequently at the thoracic and lumbosacral levels. Dorsalgia of nocturnal predominance is the main symptom and the signs of compression myelopathy are the least frequent. Diagnosis requires imaging studies such as computed tomography (CT) and magnetic resonance imaging (MRI). The treatment is surgical and according to histopathology will define adjuvant therapy. We present a patient with chronic dorsalgia and left hemiparesis; where MRI showed a T1-T3 tumor lesion, and surgical resection with a histopathological report of chondrosarcoma grade II was performed.(AU)


Assuntos
Humanos , Masculino , Feminino , Coluna Vertebral , Condrossarcoma , Neoplasias
19.
Rio de Janeiro; s.n; 2017. 100 p.
Tese em Português | LILACS, Coleciona SUS | ID: biblio-1178041

RESUMO

O condrossarcoma é um tumor ósseo maligno proveniente de cartilagem hialina. É o segundo tumor primário do osso mais frequente com 20% dos casos, sendo mais frequente em homens do que em mulheres entre a terceira e sexta década de vida. O diagnóstico é feito através de radiografia, tomografia e biópsia, onde no exame histopatológico é evidente o aumento de celularidade, núcleos aumentados e células binucleadas. O tumor é classificado em graus 1 (G1), 2 (G2), 3 (G3), desdiferenciado, mesenquimal e de células claras. O tratamento é feito através de cirurgia, pois a maioria dos condrossarcomas não responde bem a quimioterapia e radioterapia. O objetivo deste estudo foi realizar uma avaliação epidemiológica retrospectiva dos pacientes com condrossarcoma tratados no INTO e identificar se o tempo de início dos sintomas até o diagnóstico tem influência na escolha do método cirúrgico para tratamento desses pacientes. Foram avaliados 65 pacientes de ambos os sexos, com a faixa etária variando entre 6 e 86 anos e com idade média de 50 anos. Identificamos 47 (72,3%) lesões acometendo o esqueleto apendicular e 18 (27,7%) o esqueleto axial. O tempo de diagnóstico destes pacientes variou de 1 a 108 meses, como uma média de 20,5 meses. Nós observamos que o tempo de diagnóstico não influenciou no tipo cirúrgico escolhido Entretanto, verificamos que o maior impacto sobre a escolha do tipo de tratamento cirúrgico foi do estadiamento (P<0,001), com consequência na taxa de cirurgia radical especialmente nos pacientes com condrossarcoma com estadiamento IIB e III. O conjunto destes dados nos permite concluir que o tempo prolongando de diagnóstico não influencia no tipo de tratamento cirúrgico adotado e nem na incidência de metástase e mortalidade dos pacientes avaliados em nosso estudo


Chondrosarcoma is a malignant bone tumor, originating from hyaline cartilage being the second most frequent primary bone tumor with 20% of the cases, is more frequent in men than in women between the third and sixth decade of life. The diagnosis is made by radiography, tomography and biopsy, where the histopathological examination evidences the increase of cellularity, enlarged nuclei and binucleate cells, the chondrosarcomas are divided into G1, G2, G3, dedifferentiated, mesenchymal and clear cells. Treatment has done through surgery, as most chondrosarcomas do not respond well to chemotherapy and radiation therapy. The objective of this study was to conduct a retrospective epidemiological evaluation of patients with chondrosarcoma treated at INTO and to identify whether the time from onset of symptoms to diagnosis delay has influence on the choice of surgical method performed for treatment of these patients. We evaluated 65 patients of both gender, ranging in age from 6 to 86 years, with a mean age of 50 years. We identified 47 (72.3%) lesions affecting the appendicular skeleton and 18 (27.7%) the axial skeleton. The time of diagnosis of these patients ranged from 1 to 108 months, as an average of 20.5 months. We observed that the time of diagnosis did not influence the surgical type performed (P <0.92). However, it was verified that the major impact on the type of surgical treatment was patient staging (P <0.001), with a Radical surgery especially in patients stage IIB and III. All these data allow us to conclusion that the prolonged time of diagnosis does not influence the type of surgical treatment chosen and in incidence of metastasis and mortality of the patients evaluated in our study


Assuntos
Neoplasias Ósseas/diagnóstico , Condrossarcoma , Metástase Neoplásica/tratamento farmacológico
20.
Revista crea ciencia ; 10(1): 34-40, jun. 2016. ilus
Artigo em Espanhol | BISSAL, LILACS | ID: biblio-1373002

RESUMO

Se presenta el caso de un paciente masculino de la tercera década de la vida, con historia clínica de una tumoración pétrea en parrilla costal izquierda, de dos años de evolución, de crecimiento progresivo, con antecedentes familiares de exostosis hereditaria múltiple (EHM). Se exponen los estudios de imágenes e histopatológicos, haciendo una correlación que estableció el diagnóstico definitivo de condrosarcoma de bajo grado (grado I) originado en un osteocondroma del tipo similar a coliflor.


Assuntos
Exostose Múltipla Hereditária , Condrossarcoma
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