RESUMO
Gastroschisis is a rare anomaly and is usually not associated with any other congenital anomalies. The embryology of gastroschisis and omphalocele remains a matter of speculation. Incidences of gastroschisis are particularly high among pregnancies in very young women. The present case is reported because of its rare association with the condition of gastroschisis, disrupted omphalocele, with aplasia of the foot and external genital organs, as well as imperforate anus with distal rectal atresia.
Assuntos
Humanos , Gastrosquise , Hérnia Umbilical , Trinidad e TobagoRESUMO
This cross-sectional study documents the frequent occurrence of umbilical hernias among Jamaican children and suggests, for the first time, that the prescence of an umbilical hernia may be associated with larger anterior fontanelle dimensions. It also demonstrates that data about the people a community health officer serves can be recorded during a busy clinic schedule. (AU)
Assuntos
Humanos , Recém-Nascido , Lactente , Pré-Escolar , Hérnia Umbilical/epidemiologia , Crânio/crescimento & desenvolvimento , Cefalometria , Estudos Transversais , JamaicaRESUMO
A review is presented of 156 children admitted to hospital with gastro-intestinal obstruction. The common underlying causes were obstructed hernia (46.8 percent), intussusception (23.7 percent) and pyloric stenosis (16 percent) of cases. There was a marked male proponderance in each of these three groups, and the predominance of patients of African extraction in the hernia group reached 100 percent when the hernia was umbilical. Well-known observations in children with obstructed inguinal hernias which were confirmed were a right-sided prediliction, and a tendency for tecurrent obstruction in the absence of early repair. All of the patients with intussusception were under the age of one year, and this was associated with an unusually low incidence of discomfort or irritability as a presenting complaint, and a paucity of anatomical lead points. Fifteen bowel resections were required in 14 children, seven for gangrenous or irreducible intussusceptions. There were nine fatalities, four in the group with intussusception, and the details of these suggest that all fatalities could be eliminated with improvements in respiratory care, and pre-and intra-operative management (AU)
Assuntos
Criança , Pré-Escolar , Feminino , Humanos , Lactente , Masculino , Obstrução Intestinal/etiologia , Fatores Etários , Hérnia Inguinal/complicações , Hérnia Inguinal/mortalidade , Hérnia Umbilical/complicações , Hérnia Umbilical/mortalidade , Obstrução Intestinal/mortalidade , Intussuscepção/complicações , Intussuscepção/mortalidade , Estenose Pilórica/complicações , Estenose Pilórica/mortalidade , Fatores Sexuais , Trinidad e TobagoRESUMO
The clinical and laboratory findings in six Jamaican infants with the exomphalos-macroglossia-gigantism syndrome are described. The incidence was calculated as 1:13,700 births. There was no family history of similar disease in any case and no evidence of chromosomal abnormality, virus infection, or infantile hypoglycemia. Three infants died, and two showed typical histological features in the kidneys and adrenal glands.(AU)
