Multiple lentigines syndrome in Dominica

Multiple Lentigines Syndrome with variable penetrance is described in a Dominican family mild skeletal manifestations, including arachnodactyly, were present with low intellect in the propositus. The syndrome is of importance because of the association with various cardiac abnormalities and deafness. It occurs in black people though the lentigines may be difficult to recognise, and relatives without lentigines may have cardiac abnormalities (AU)