Ofuji disease: a rare dermatosis and its challenging therapeutic approach
An. bras. dermatol
; 91(5): 646-648, Sept.-Oct. 2016. graf
Article
in En
| LILACS
| ID: biblio-827753
Responsible library:
BR1.1
ABSTRACT
Abstract Eosinophilic pustular folliculitis (EPF) or Ofuji disease is a rare dermatosis, prone to recurrence and chronicity. The peak incidence occurs in the third decade of life and its exact etiology remains unknown. Evidence suggests that the expression of adhesion molecules and the production of cytokines activate the follicular unit, but the stimulus that triggers these changes remains unclear. The three clinical variants reported in the literature include classic EPF, immunosuppression-associated EPF, and infancy-associated EPF. We report a case of eosinophilic pustular folliculitis with peculiar epidemiological characteristics, which represents a challenging therapeutic scenario.
Key words
Full text:
1
Collection:
01-internacional
Database:
LILACS
Main subject:
Pregnancy Complications
/
Anti-Inflammatory Agents, Non-Steroidal
/
Indomethacin
/
Skin Diseases, Vesiculobullous
/
Eosinophilia
/
Folliculitis
Limits:
Adult
/
Female
/
Humans
Language:
En
Journal:
An. bras. dermatol
Journal subject:
DERMATOLOGIA
Year:
2016
Document type:
Article
Affiliation country:
Brazil
Country of publication:
Brazil