RESUMO
Hemangiopericytomas are rare mesenchymal lesions arising from pericytes within the walls of capillaries. They often have an unpredictable course. We present a case of a large retroperitoneal hemangiopericytoma in a 65-year-old woman who initially presented with upper gastrointestinal discomfort. Following exptirpative surgery, pathology was consistent with hemangiopericytoma of low malignant potential. Widespread metastasis was discovered on follow up imaging, 17 months following surgery. To our knowledge, this is the first case report demonstrating a primary retroperitoneal hemangioperictoma with confirmed metastases.
Assuntos
Hemangiopericitoma/secundário , Neoplasias Hepáticas/secundário , Neoplasias Pulmonares/secundário , Neoplasias Retroperitoneais/patologia , Neoplasias da Coluna Vertebral/secundário , Idoso , Evolução Fatal , Feminino , Hemangiopericitoma/cirurgia , Humanos , Neoplasias Hepáticas/diagnóstico , Neoplasias Pulmonares/diagnóstico , Imageamento por Ressonância Magnética , Neoplasias Retroperitoneais/cirurgia , Neoplasias da Coluna Vertebral/diagnósticoRESUMO
We present a case of an ectopic renal tumor in a 61-year-old morbidly obese man with a pelvic kidney found after presenting with hematuria and irritative voiding symptoms. The mass, along with the ectopic kidney and ureter, was radically resected through an open operation that involved removing both them and the renal vessels from the underlying iliac vessels. Pathological analysis demonstrated an 8.3 cm papillary renal cell carcinoma (RCC) with oncocytic features, Fuhrman nuclear grade 3, with angiolymphatic invasion and negative margins. The patient has been recurrence-free for over four years since tumor resection.