1.
Rev Port Cardiol
; 35(3): 185.e1-4, 2016 Mar.
Artigo
em Português
| MEDLINE
| ID: mdl-26928017
RESUMO
Left ventricular noncompaction is a rare congenital anomaly characterized by excessive left ventricular trabeculation, deep intertrabecular recesses and a thin compacted layer due to the arrest of compaction of myocardial fibers during embryonic development. We report the case of a young patient with isolated left ventricular noncompaction, leading to refractory heart failure that required extracorporeal membrane oxygenation followed by emergency heart transplantation.
Assuntos
Cardiopatias Congênitas/complicações , Insuficiência Cardíaca/etiologia , Transplante de Coração/efeitos adversos , Ventrículos do Coração , Humanos
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