Type 1 diabetes and idiopathic retroperitoneal fibrosis: case report.
Ann Endocrinol (Paris)
; 70(2): 129-32, 2009 Apr.
Article
em En
| MEDLINE
| ID: mdl-18995843
ABSTRACT
Retroperitoneal fibrosis is characterized by the presence of a retroperitoneal tissue, consisting of chronic inflammation and marked fibrosis, which entraps the retroperitoneal organs. In two-thirds of cases, the retroperitoneal fibrosis is idiopathic. The pathogenic mechanism is not clearly identified. We report a case of idiopathic retroperitoneal fibrosis associated with type 1 diabetes mellitus. A 61-year-old woman with C peptide negative insulindependent diabetes developed retroperitoneal fibrosis revealed by bilateral hydronephrosis. Anti-GAD 65 antibodies were positive. There were no signs of autoimmune pancreatitis no steatorrhea, normal IgG4 isotype levels, and absence of pancreas morphological abnormalities.
Texto completo:
1
Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Fibrose Retroperitoneal
/
Diabetes Mellitus Tipo 1
Tipo de estudo:
Prognostic_studies
Limite:
Female
/
Humans
/
Middle aged
Idioma:
En
Revista:
Ann Endocrinol (Paris)
Ano de publicação:
2009
Tipo de documento:
Article
País de afiliação:
França