Sinus of valsalva aneurysm in Blau's syndrome.
J Cardiothorac Surg
; 5: 16, 2010 Mar 26.
Article
em En
| MEDLINE
| ID: mdl-20346129
ABSTRACT
Blau syndrome is a rare granulomatous disorder inherited in an autosomal dominant manner characterized by the early appearance of granulomatous arthritis, skin rash and anterior uveitis. There are very few data on the cardiovascular manifestations of Blau syndrome. Here we report the first case of sinus of valsava aneurysm in Blau syndrome. In isolated unruptured aneurysms of a sinus of Valsalva without compromise of the aortic valve and/or the coronary ostia, repair may be accomplished by simple placation of the aneurysm or excision of the aneurysm(s) and patch closure of the defect(s) between the aortic annulus and the sinu-vascular ridge. Because of the particular conditions in our case, the repair was performed with replacement of the aortic valve and root using a composite graft employing a modified Bentall's technique.
Texto completo:
1
Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Aneurisma Aórtico
/
Seio Aórtico
/
Dermatopatias
/
Doença Granulomatosa Crônica
Tipo de estudo:
Diagnostic_studies
Limite:
Adult
/
Female
/
Humans
Idioma:
En
Revista:
J Cardiothorac Surg
Ano de publicação:
2010
Tipo de documento:
Article
País de afiliação:
Reino Unido