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An Engineered sgsh Mutant Zebrafish Recapitulates Molecular and Behavioural Pathobiology of Sanfilippo Syndrome A/MPS IIIA.
Douek, Alon M; Amiri Khabooshan, Mitra; Henry, Jason; Stamatis, Sebastian-Alexander; Kreuder, Florian; Ramm, Georg; Änkö, Minna-Liisa; Wlodkowic, Donald; Kaslin, Jan.
Afiliação
  • Douek AM; Australian Regenerative Medicine Institute, Monash University, Clayton, VIC 3800, Australia.
  • Amiri Khabooshan M; Australian Regenerative Medicine Institute, Monash University, Clayton, VIC 3800, Australia.
  • Henry J; Neurotoxicology Lab, School of Science (Biosciences), RMIT University, Bundoora, VIC 3083, Australia.
  • Stamatis SA; Australian Regenerative Medicine Institute, Monash University, Clayton, VIC 3800, Australia.
  • Kreuder F; Australian Regenerative Medicine Institute, Monash University, Clayton, VIC 3800, Australia.
  • Ramm G; Ramaciotti Centre for Cryo-Electron Microscopy, Monash University, Clayton, VIC 3800, Australia.
  • Änkö ML; Department of Biochemistry and Molecular Biology, Biomedicine Discovery Institute, Monash University, Clayton, VIC 3800, Australia.
  • Wlodkowic D; Centre for Reproductive Health and Centre for Cancer Research, Hudson Institute of Medical Research, Clayton, VIC 3168, Australia.
  • Kaslin J; Department of Molecular and Translational Sciences, Monash University, Clayton, VIC 3800, Australia.
Int J Mol Sci ; 22(11)2021 May 31.
Article em En | MEDLINE | ID: mdl-34073041

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Mucopolissacaridose III / Modelos Animais de Doenças / Hidrolases Limite: Animals / Humans Idioma: En Revista: Int J Mol Sci Ano de publicação: 2021 Tipo de documento: Article País de afiliação: Austrália

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Mucopolissacaridose III / Modelos Animais de Doenças / Hidrolases Limite: Animals / Humans Idioma: En Revista: Int J Mol Sci Ano de publicação: 2021 Tipo de documento: Article País de afiliação: Austrália