Rare association of tetralogy of Fallot with partially unroofed coronary sinus and PLSVC: case report.

ABSTRACT

A 41-year-old man with tetralogy of Fallot and dextrocardia, coronary sinus atrial septal defect and partially unroofed coronary sinus with persistent left superior vena cava (PLSVC) underwent a total correction of these anomalies. An association between these specific anomalies has not been reported previously in the literature. These defects were successfully corrected by a) closure of the coronary sinus atrial septal defect with PLSVC entering the right atrium using a pericardial graft; and b) ventricular partition with a Dacron patch and conotruncal repair for tetralogy of Fallot. The postoperative course of this patient has been uneventful.