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Déficit de proteína C en un paciente con coagulación intravascular diseminada asociada a sepsis y trombosis venosa profunda: Case report. / [Protein C deficiency in patient with sepsis-associated disseminated intravascular coagulation and deep vein thrombosis].

Tassin Mauro; Llarena Pablo; Laffaye Federico; Kaltenbach Germán.
Arch Argent Pediatr ; 111(1): e28-30, 2013 Jan-Feb.
Artículo en Español | BINACIS | ID: bin-133190
Disseminate intravascular coagulation (DIC) is a clinical pathological syndrome associated to several diseases. Sepsis is the most common cause in infants and children. DIC results from the anomalous activation of blood coagulation, widespread formation of thrombi in the microcirculation, and consumption of clotting factors and platelets. Clinical findings are variable; the most common is bleeding, followed by purpura and acral gangrene (purpura fulminans). We report a patient with sepsis associated-DIC and concurrent deep venous thrombosis. The diagnostic evaluation allowed to discover inherited thrombophilia associated to protein C deficiency.