[Idiopathic hepatic angiosarcoma. A case report]. / Angiosarcoma hepático idiopático. Informe de un caso.

Hepatic angiosarcoma is a malignant mesenchymal neoplasm of endothelial cells of high grade. Hepatic angiosarcoma represents two percent of all primary neoplasm liver. The highest incidence is between the sixth and seventh decade of life, youth and children is rare, predominantly in men (3:1). Most are idiopathic (75 %). Diagnosis is difficult because clinical manifestations and imaging studies are inconclusive. When clinical manifestations begin progression is often fast, and possibilities for curative treatment are limited. We report the case of a man aged 17, presented two clinical episodes of hemoperitoneum with ultrasound and CT diagnosis of hepatic hemangioma, hepatectomy was performed in the right lobe, the histological study reported multicenter liver angiosarcoma.

[Clear cells cervical adenocarcinoma in a girl no exposed to dietiletilbestrol]. / Adenocarcinoma de células claras de cérvix en niña no expuesta a dietiletilbestrol.

BACKGROUND: the clear cell adenocarcinoma (CCA) in cervix is a rare disease. It represents only 2 to 7 % of whole adecocarcinomas of cervix. Its histological pattern seems identical to their counterparts elsewhere in the female genital tract, including the vagina, endometrial and ovary. The CCA is constituted by cells with a clear cytoplasm in tack that are arranged in a solid pattern, tubu-locystic, papillary, or mixed. CLINICAL CASE: an eleven year old girl with sporadic and intermittent transvaginal bleeding, and who felt in severe anemia due to hiperpolimenorrea treated with athinyl estradiol deso-gestrel was attended. She had not history of exposition in utero to diethyletilbestrol. Hysteroscopy showed an ectocervical exophytic lesion in a barrel of 7 × 3 × 3 cm, located predominantly in the posterior lip. A frozen section of the lesion was reported as a poorly differentiated malignant tumor compatible with cervical carcinoma. She underwent to simple trachelectomy. CONCLUSIONS: diagnostic difficulty was the age of the patient and the lack exposition in utero to DES, the differential diagnosis included the age group tumors and rhabdomyosarcoma botryoides and extragonadal endodermic origen with papillary and reticular pattern. Another was a metastatic CCA.

[Abdominal wall soft tissue perineurioma. Autopsy findings and review of the literature]. / Perineuroma de tejidos blandos en pared abdominal. Hallazgos anatomopatológicos y revisión de la literatura.

The perineuroma is a rare benign tumor, derived from nerve sheath perineurial cells. It was first described in 1978 by Lazarus and Trombetta, who based their diagnosis on the ultrastructural features of perineurioma cells. Subsequently, the immunohistochemical profile of perineurial cells allowed an easier diagnosis of this condition. A case of perineurioma in a 47-year-old woman is reported. The patient presented with an abdominal wall mass, with aprevious diagnosis of malignant fibrous histiocytoma (MFH). The case was reviewed at an oncology hospital, inmunohistochemistry was performed and the concluding diagnosis was soft tissue perineurioma.