Bronchopulmonary dysgenesis

The experience with the diagnosis and treatment of bronchopulmonary dysgenesis is presented. Twenty-eight patients were evaluated: 8 with congenital lobar emphysema; 9 with bronchial cyst; 4 with adenomatoidcystic malformation; 4 with pulmonary sequestration; 2 patients with arteriovenous malformation; and 1 pulmonary agenesia. Two patients died in the postoperative period (7.6 percent of postoperative mortally). Two were not operated on, and the remainder had a satisfactory outcome following sugery. The complications and the follow-up of the patients are analyzed. Embriologic considerations are made and the diagnostic and surgical methods used are evaluated.