RESUMEN
A young man presented to the emergency department with pleuritic chest pain and shortness of breath. Of note, he recently went on a long-distance flight of about 9 hours. Given his recent long-distance travel and clinical symptoms, a pulmonary embolism was suspected. However, pathological examination of the excised pulmonary artery intraluminal mass demonstrated an angiomatoid fibrous histiocytoma. This case describes the clinicopathological and immunohistochemical features and molecular profile of a rare type of pulmonary artery tumour, a pulmonary artery angiomatoid fibrous histiocytoma.
Asunto(s)
Histiocitoma Fibroso Benigno , Histiocitoma Fibroso Maligno , Embolia Pulmonar , Masculino , Humanos , Arteria Pulmonar/diagnóstico por imagen , Arteria Pulmonar/patología , Histiocitoma Fibroso Benigno/patología , Embolia Pulmonar/diagnóstico , Histiocitoma Fibroso Maligno/diagnóstico , Histiocitoma Fibroso Maligno/cirugía , Histiocitoma Fibroso Maligno/patologíaRESUMEN
We present a case of a 29-year-old female with fragility fracture of the ninth thoracic vertebrae with a z-score of -3.3 of the lumbosacral spine. She was worked up for secondary causes of osteoporosis, all of which was unrevealing except for a low vitamin D level which was repleted. She had genetic profile done, which revealed low-density lipoprotein receptor-related 5 mutation which was thought to the cause of premature osteoporosis. This report highlights a rare case of osteoporosis in a premenopausal female and challenges associated with premenopausal osteoporosis.
