RESUMEN
We present a case of a premature infant with a presumed obstructive uropathy found to be a megalourethra leading to a perinatal postrenal failure. A megalourethra - an uncommon cause of urethral dilatation - is a congenital, non-obstructive anomaly of the penile erectile tissue. We think that a distal stenosis resulted in dysplasia of the penile tissue and an aspect of a megalourethra. Further diagnostic workup included urinary tract sonograms, a voiding cystourethrogram and MAG3 scintigrafy. Initially the patient was managed with supportive care such as a suprapubic urinary catheter, followed by surgical intervention (Bengt Johanson).
Asunto(s)
Enfermedades del Prematuro/etiología , Atención Perinatal , Insuficiencia Renal/etiología , Uretra/anomalías , Dilatación Patológica/congénito , Dilatación Patológica/diagnóstico , Dilatación Patológica/cirugía , Estudios de Seguimiento , Humanos , Lactante , Recién Nacido , Enfermedades del Prematuro/diagnóstico , Masculino , Insuficiencia Renal/diagnóstico , Insuficiencia Renal/cirugía , Tecnecio Tc 99m Mertiatida , Uretra/cirugía , Vejiga Urinaria/anomalías , Retención Urinaria/diagnóstico , Retención Urinaria/etiología , UrografíaRESUMEN
We report a 12-year-old girl with a long history of constant urinary dribbling and apparently only a left kidney. Using a multimodality approach involving the fusion of MR urography and (99m)Tc-dimercaptosuccinic acid (DMSA) SPECT datasets, it was finally possible to exactly localize the very small dystopic, dysplastic right kidney and its ectopic ureter draining into the vagina.
