RESUMEN
Placoid pigment epitheliopathy and serpiginous choroiditis are among the white dot retinal syndromes and possess similarities that can cause confusion between these two diseases. However, they are very different in terms of their progression and prognosis, which requires a diagnosis of certainty in order to better manage the patients with the diseases and identify potentially serious progressive complications. The clinical presentation, results of testing, differential diagnoses and treatment of these two pathologies are discussed in this article.
Asunto(s)
Epitelio Pigmentado Ocular/patología , Enfermedades de la Retina , Síndromes de Puntos Blancos , Coroiditis/diagnóstico , Coroiditis/patología , Coroiditis/terapia , Diagnóstico Diferencial , Progresión de la Enfermedad , Humanos , Trastornos de la Pigmentación/diagnóstico , Trastornos de la Pigmentación/patología , Trastornos de la Pigmentación/terapia , Pronóstico , Enfermedades de la Retina/diagnóstico , Enfermedades de la Retina/patología , Enfermedades de la Retina/terapia , Síndromes de Puntos Blancos/diagnóstico , Síndromes de Puntos Blancos/terapiaRESUMEN
Placoid pigment epitheliopathy and serpiginous choroiditis are among the white dot retinal syndromes and possess similarities that can cause confusion between these two diseases. However, they are very different in terms of their progression and prognosis, which requires a diagnosis of certainty in order to better manage the patients with the diseases and identify potentially serious progressive complications. The clinical presentation, results of testing, differential diagnoses and treatment of these two pathologies are discussed in this article.
Asunto(s)
Enfermedades de la Retina , Epitelio Pigmentado de la Retina/patología , Síndromes de Puntos Blancos , Diagnóstico Diferencial , Progresión de la Enfermedad , Humanos , Pronóstico , Enfermedades de la Retina/diagnóstico , Enfermedades de la Retina/epidemiología , Enfermedades de la Retina/patología , Enfermedades de la Retina/terapia , Resultado del Tratamiento , Síndromes de Puntos Blancos/diagnóstico , Síndromes de Puntos Blancos/epidemiología , Síndromes de Puntos Blancos/patología , Síndromes de Puntos Blancos/terapiaRESUMEN
The white dot syndromes include a group of diseases which are characterized by multiple yellowish-white foci in the outer retina, retinal pigment epithelium, and choroid. For clinicians and researchers alike they present significant diagnostic and therapeutic challenges. White dot syndromes include primary inflammatory choriocapillaropathies, such as acute posterior multifocal placoid pigment epitheliopathy (APMPPE)/acute multifocal ischemic choriocapillaropathy (AMIC), multiple evanescent white dot syndrome (MEWDS)/acute idiopathic blind spot enlargement (AIBSE), multifocal choroiditis (MFC), punctate inner choroidopathy (PIC), serpiginous choroiditis (SC), acute zonal occult outer retinopathy (AZOOR), and acute macular neuroretinopathy (AMN). Among the primary stromal choroiditis is birdshot retinochoroidopathy (BSRC); however, the pathogenesis of these disorders is largely unknown. Immunological reactions to previous viral infections with a genetic disposition seem to be a common denominator.