Melkersson-Rosenthal syndrome associated with Down syndrome.

We present a clinical case of Melkersson-Rosenthal (M-R) syndrome associated with Down syndrome. No evidence of this association is described in the literature. We also present a technique for the macrocheilia treatment of lower lip caused by M-R syndrome in a patient with Down syndrome. This patient during pediatric age had many events of facial nerve paralysis and edematous episodes of lower lip with unknown etiology. This technique is based on a wedge full thickness central excision of the lower lip and on a transversal lozenge excision in the vermilion portion with orbicular muscle to reverse the chin-labial corner. The results are an agreeable aspect of the lip and physiological digestive and phonetic processes. The technique is safe and simple and the aesthetic functional result is very good. In our case, the postoperative complication is caused by an insufficient collaboration of the patient and it is solved in three weeks.

Rare malignant tumors of the scalp: a report of four cases, their treatment and a review of the literature.

BACKGROUND AND OBJECTIVES: Malignant tumors occurring in the scalp are not common and when asymptomatic or small in size, may be covered by hair and neglected by the patient, leading to a potential risk of delay in detection and resulting in poorer outcomes. MATERIALS AND METHODS: In our Departments in the last five years more than 200 malignant tumors of the scalp have been operated on. In this article we take into consideration four rare malignant tumours of the scalp taken from this study: a giant recurrent sebaceous carcinoma, a lung cancer metastatic lesion, a malignant melanoma and a breast cancer metastasis. RESULTS: The four patients with rare malignant tumours have been operated with good results. DISCUSSION: These four cases represent an important lesson for the plastic surgeon to learn: in the case of the presence of unusual, ulcerated/pigmented lesion of the scalp or in the case of alopecia we must consider the possibility of a tumour.

The importance of peritoneal imaging in the workup of genital edema in patients on continuous ambulatory peritoneal dialysis.

BACKGROUND: Genital edema is a well-reported complication of peritoneal dialysis. This phenomenon has been associated with extravasation of dialysate from the peritoneal cavity through a defect in the abdominal wall or through an wall or through an inguinal hernia (or patent processus vaginalis, persistent sac). In the first case, fluid tracks through the soft tissues of the abdominal wall and settles in the dependent genitalia. In the second, fluid tracks through the inguinal hernial defect and infiltrates into the tissues distal to the defect. It is difficult to precisely diagnose the etiology of many of these cases but it is obviously important. METHOD: We report a case of a patient who presented with penile and scrotal edema and was eventually found to have bilateral patent processus vaginalae. We used computed tomography and peritoneal scintigraphy in order to ascertain the diagnosis. RESULTS/CONCLUSIONS: We believe that computed tomography and peritoneal scintigraphy are extremely helpful in the workup of genital edema in patients on continuous ambulatory peritoneal dialysis.

A comparison of the long-pulse and short-pulse Alexandrite laser hair removal systems.

Laser-assisted hair removal has been reported previously with the Nd:YAG laser, the long-pulse ruby laser, the long-pulse Alexandrite laser, and the short-pulse Alexandrite laser. Results with all these lasers have been successful; however, it has been postulated that the long-pulse Alexandrite laser would have a lower complication rate and greater efficacy at identical fluences than the short-pulse Alexandrite laser. The authors chose to compare directly the pulsed Alexandrite lasers for speed of application, complications, and results. Eighteen patients who desired hair removal were entered into the study. There were 10 female and 8 male patients, with a mean age of 36 years. All skin types from Fitzpatrick classes I through VI were treated. The body areas treated consisted of the face, ears, neck, back, arms, upper thighs, bikini lines, legs, and breasts. One side of the body was treated with the short-pulse (2-msec) Alexandrite laser (Sharplan Epitouch 5100). The other half was treated with a long-pulse (20-msec) Alexandrite laser. Both lasers were set at the same fluence for each patient. Patients reported a 60% to 80% reduction in hair growth at 6 months. Both sides were identical with regard to return of hair growth and complications such as hypopigmentation. Both the long- and short-pulse Alexandrite laser systems yielded an effective method of hair reduction with minimal complications. Equal results and complications were obtained with the two systems. The only exception was that the length of the procedure was shorter with the short-pulse Alexandrite laser.

Complications of subcutaneous injection ports.

Subcutaneous injection ports have become widely used for patients who require prolonged central venous access. Complications of their placement and use are well documented in the existing literature. We report two previously undocumented complications occurring in Port-a-Cath units, and suggest methods to lessen the likelihood of recurrence of these problems.

Photographic standards in plastic surgery.

Standard photographic technique in plastic surgery is an important topic that has been stressed in the discipline over the past several years. Clinical photographs should always be taken with the same camera lens, lens setting, lighting, film, and patient position to ensure reproducibility and to enable valid pre- and postoperative comparisons. A 35-mm single lens reflex camera is highly recommended for this type of photography. Two lenses are suggested, one with a focal length range of 50 to 60 mm and one with a focal length range of 90 to 105 mm. Both should have macro capability. Two or more flash units are recommended, either camera-mounted or a studio system set-up in the office. Using the patient preparation method and technique outlined in the text, the Standards in Clinical Photography achieve consistency from patient to patient and also in the same patient in pre- and postoperative photographs. Henceforth, the information discussed in the article forms the basis for standard views, regardless of the image-capture medium.

Laparoscopic splenectomy in a Jehovah's Witness with profound anemia.

Open surgery in a severely anemic patient may be complicated by a substantial blood loss from a large incision and subsequent poor wound healing secondary to the anemia. We report our success in performing a splenectomy laparoscopically in a profoundly anemic patient. A 50-year-old white male Jehovah's Witness who was HIV positive was referred for splenectomy after he developed profound, worsening anemia secondary to hypersplenism that was refractory to medical management. His preoperative hemoglobin and hematocrit levels were 2.7 g/dl and 8.8%, respectively, but his religious beliefs precluded transfusion. A laparoscopic splenectomy by the posterior gastric approach was performed. The patient tolerated the surgery well and experienced no additional morbidity. On postoperative day 7, his hemoglobin and hematocrit were 6.8 g/dl and 22%, respectively. We conclude that laparoscopic splenectomy is an attractive procedure in a severely anemic patient who requires splenectomy and refuses blood transfusion.

Chief resident experience with laparoscopic cholecystectomy.

Resident competence in both open and laparoscopic cholecystectomy (LC) has been a concern among general surgeons. Laparoscopic surgery was late in coming at many surgical residency programs in the United States, and many residents have graduated with limited experience in LC. We are chief residents who were fortunate enough to start our training when LC was first introduced at our institution in 1990. This report summarizes our experience with LC in our chief year, during which we performed LC on 147 patients. The average operating time was 37 minutes (range, 12-82 minutes). Six patients (4%) required conversion to an open procedure. There were three complications (2 postoperative cystic duct leaks and 1 intraoperative common bile duct injury) for an overall complication rate of 2%. There was no mortality. It is our conclusion that graduating chief residents with 5 years' exposure to LC may perform the procedure with a complication rate comparable to that reported in the current literature. Insuring that graduating chief residents have adequate training in open cholecystectomy may become a more pressing issue in the near future.

A simplified approach to laparoscopic fundoplication.

BACKGROUND: There is a certain amount of controversy regarding the need to divide the short gastric vessels (SGV) in laparoscopic fundoplication for treatment of gastroesophageal reflux disease (GERD). In addition, there is often difficulty in identifying the crural fibers when encircling the lower esophagus. METHODS: We determine whether it is necessary to divide the SGV by trying to appose the gastric fundus to the anterior abdominal wall intraoperatively. If this could be done easily, the SGV are preserved. When their division is required, a posterior gastric approach is employed. We have also found that the injection of methylene blue into the left crural fibers anterior to the esophagus is helpful in identifying the left side when dissection posterior to the gastroesophageal junction is difficult. RESULTS: Between 1992 and 1995 we performed 20 laparoscopic fundoplications for GERD. All patients had at least grade 3 esophagitis (Savary-Miller scale), increased esophageal exposure to acid (median DeMeester score of 195), and decreased lower esophageal sphincter (LES) pressure. The median operative time was 175 min. There were no conversions to open surgery, and there was no mortality. Three patients developed transient postoperative dysphagia and one patient had pneumonia. The median hospital stay was 3 days; all patients were free of reflux symptoms at follow-up ranging from 7 to 42 months. CONCLUSION: We conclude that the techniques described by us aid in intraoperative decision making and allow laparoscopic fundoplication to be both simple and effective.

Pneumothorax as a complication of laparoscopic inguinal hernia repair.

Pneumothorax was identified as a complication of endoscopic hernia repair in two patients with insufflation pressures of 15 mmHg and operating times exceeding 2 h. These patients also showed intraoperative perturbations in both oxygen saturation and end-tidal CO2 production. A prospective study was undertaken to determine whether similar complications would arise if preperitoneal insufflation pressures were limited to 10 mmHg. Postoperative chest x-rays were obtained on all patients to check for pneumothoraces, even clinically occult ones. Fifty patients were studied, with average operating times of 67 min. No patient demonstrated any hemodynamic or ventilatory changes, and none had any evidence of pneumothorax on x-ray. We conclude that these complications were not present when insufflation pressure was maintained at 10 mmHg and that routine x-ray is not warranted. Larger randomized trials of insufflation pressures are needed.

Laparoscopic staging of Hodgkin's disease.

With recent advances in laparoscopy, specifically the development of laparoscopic splenectomy, a complete laparoscopic Hodgkin's staging procedure is now possible. Using five trocars and the patient in the right semidecubitus position, six laparoscopic staging procedures were performed. All were stages IIA or IIB pre-operatively, and none were upgraded to stage III or IV as a result of the procedure. Operative time was from 185-255 min. (mean 210 min.) There were no operative morbidities or mortalities associated with the procedure. We believe this procedure will be adopted by more surgeons as they become more comfortable in performing laparoscopic splenectomies.

Endoscopic extraperitoneal herniorrhaphy in 316 patients.

The posterior approach for groin hernia repair as popularized by Stoppa and Nyhus is one of the most solid repairs available. It requires a larger incision than the anterior approach, which has limited its use to recurrent and bilateral hernias. The endoscopic extraperitoneal herniorrhaphy (EEPH) accomplishes a similar repair via three minute incisions. This study suggests that EEPH is at least as safe and efficient as the open preperitoneal repair. Three hundred sixteen male patients underwent 405 hernia repairs by an endoscopic extraperitoneal approach. Ages ranged from 18 to 82 years old. There were 204 indirect, 182 direct, 13 pantaloon, and six femoral hernias. Eighty-nine were bilateral and 42 were recurrent. All repairs were done using polypropylene mesh. Follow-up has been achieved in 89% of patients and ranged from 7 to 50 months, with a median of 25 months. Seven patients (2.2%) required conversion to an open approach. Five recurrences have developed to date. Complications (5.7%) have included urinary retention, bladder injury, groin and/or scrotal hematoma, trocar site infection, lateral femoral cutaneous nerve neuralgia, and cardiac arrhythmia. Endoscopic extraperitoneal herniorrhaphy may provide an appropriate alternative to other methods of hernia repair when performed by experienced laparoscopists.

149 ambulatory laparoscopic cholecystectomies.

BACKGROUND: The purpose of this study was to compare ambulatory laparoscopic cholecystectomy (LC) with overnight LC and to determine its safety and the factors which will predict its success. METHODS: Ambulatory LC was defined as LC followed by less than a 12-h stay in the ambulatory surgery unit; overnight LC was defined as LC followed by a hospital admission of less than 24 h. A retrospective chart review was completed. RESULTS: One hundred forty-nine ambulatory LC, were performed in an 18-month period. Ninety-one were successful (61%); 58 patients required overnight admission for pain management, control of nausea, or their reluctance to be discharged. There were five complications and no mortalities. The duration of the surgical procedure was the only significant objective factor we could find in predicting success of ambulatory LC. CONCLUSIONS: We conclude that ambulatory LC is safe and effective in treating patients requiring cholecystectomy. The duration of the procedure and the patient's own motivation are key factors in predicting success of early discharge.

Hematuria associated with ruptured abdominal aortic aneurysms.

A retrospective study of the Staten Island University Hospital experience with ruptured abdominal aortic aneurysms (AAA) was undertaken. The study covered a 58 month period and included 30 patients. The purpose of the study was to investigate the relationship of ruptured AAA with hematuria. We specifically investigated (1) the incidence of hematuria in patients with ruptured AAA, (2) weather the presence of hematuria in these patients led to a delay in the diagnosis of ruptured AAA, and (3) if the presence of hematuria adversely effected survival as a function of causing a delay in diagnosis. The data revealed an 87% incidence of hematuria in ruptured AAA. Furthermore, gross hematuria was found to cause a statistically significant delay in arriving at the diagnosis of a ruptured AAA. This delay however could not be demonstrated to adversely affect patient survival.