RESUMO
Soft tissue sarcomas (STSs) are a heterogeneous group of rare neoplasms originating from the embryonic mesoderm and mesenchymal cells. Primary peritoneal sarcomas have been reported as leiomyosarcoma, liposarcoma and carcinosarcoma. However, primary peritoneal spindle cell sarcoma has never been reported in the literature. Herein, we report on a 38-year-old woman with massive ascites diagnosed as primary peritoneal spindle cell sarcoma. Following doxorubicin and ifosfamide chemotherapy, her symptoms improved and ascites regressed. Other primary peritoneal sarcomas rarely cause massive ascites. We suggest that in patients presenting with massive exudative ascites associated with malignancy, primary peritoneal sarcomas should be also considered in the differential diagnosis.
Assuntos
Protocolos de Quimioterapia Combinada Antineoplásica/uso terapêutico , Ascite/etiologia , Neoplasias Peritoneais/complicações , Sarcoma/complicações , Neoplasias de Tecidos Moles/complicações , Adulto , Ascite/tratamento farmacológico , Ascite/patologia , Doxorrubicina/administração & dosagem , Feminino , Humanos , Ifosfamida/administração & dosagem , Neoplasias Peritoneais/diagnóstico , Neoplasias Peritoneais/tratamento farmacológico , Prognóstico , Sarcoma/diagnóstico , Sarcoma/tratamento farmacológico , Neoplasias de Tecidos Moles/diagnóstico , Neoplasias de Tecidos Moles/tratamento farmacológico , Resultado do TratamentoAssuntos
Encefalopatias/diagnóstico por imagem , Encefalopatias/fisiopatologia , Encéfalo/diagnóstico por imagem , Encéfalo/fisiologia , Sinapses/diagnóstico por imagem , Tomografia Computadorizada de Emissão , Humanos , Transmissão Sináptica/fisiologia , Tomografia Computadorizada de Emissão de Fóton ÚnicoRESUMO
Benign neurofibromas undergo sarcomatous transformation in approximately 5% of patients with neurofibromatosis type I. The clinical and radiologic diagnosis of sarcomatous change remains difficult. Positron emission tomography with F-18 fluorodeoxyglucose is a method to assess increased glucose metabolism in malignant tissue such as sarcomas. In this case report, positron emission tomography accurately distinguished malignant from benign neurofibromas. The technique may be useful as a noninvasive screening tool for malignant transformation of neurofibromas.