Cleidocranial dysostosis: a report on two familial cases / Disostose cleidocraniana: relato de dois casos familiares
Radiol. bras
; 46(6): 382-384, Nov-Dec/2013. graf
Article
en En
| LILACS
| ID: lil-699246
Biblioteca responsable:
BR1.1
ABSTRACT
Cleidocranial dysostosis is a rare genetic syndrome with an autosomal dominant inheritance pattern. The most common manifestations include clavicular aplasia or hypoplasia, open fontanelles and abnormal dentition. The present report describes two familial cases whose late diagnosis was made by means of clinical and radiographic findings. The treatment was radical, with complete surgical teeth extraction and making of total dental prosthesis.
Texto completo:
1
Colección:
01-internacional
Base de datos:
LILACS
Idioma:
En
Revista:
Radiol. bras
Asunto de la revista:
DIAGNOSTICO POR IMAGEM
/
RADIOLOGIA
Año:
2013
Tipo del documento:
Article
País de afiliación:
Brasil