Ewing's sarcoma/primitive neuroectodermal tumor arising from the adrenal gland: a case report and literature review.
Tumori
; 99(3): e104-6, 2013.
Article
en En
| MEDLINE
| ID: mdl-24158076
ABSTRACT
We report a rare case of Ewing's sarcoma (ES)/primitive neuroectodermal tumor (PNET) arising from the adrenal gland. A 17-year-old Japanese woman presented with left upper abdominal pain and high fever. Computed tomography and magnetic resonance imaging revealed a 15 × 10 cm tumor replacing the adrenal gland. Preoperative diagnosis was an adrenocortical carcinoma. Resection of the tumor was performed. We obtained the final diagnosis of ES/PNET by immunohistochemical molecular study with positive staining for the MIC2 gene product (CD99) and a Ewing sarcoma breakpoint region 1 (EWSR1) gene rearrangement. Local recurrence was observed one month after the surgery. The patient was then treated with systemic chemotherapy and localized radiotherapy.
Texto completo:
1
Colección:
01-internacional
Base de datos:
MEDLINE
Asunto principal:
Sarcoma de Ewing
/
Proteínas de Unión a Calmodulina
/
Reordenamiento Génico
/
Antígenos CD
/
Moléculas de Adhesión Celular
/
Proteínas de Unión al ARN
/
Neoplasias de las Glándulas Suprarrenales
Tipo de estudio:
Diagnostic_studies
/
Etiology_studies
Límite:
Adolescent
/
Female
/
Humans
Idioma:
En
Revista:
Tumori
Año:
2013
Tipo del documento:
Article