Biliary atresia associated with polysplenia syndrome, dextrocardia, situs inversus totalis and malrotation of intestines.
J Neonatal Surg
; 3(1): 9, 2014.
Article
en En
| MEDLINE
| ID: mdl-26023480
ABSTRACT
Biliary atresia (BA) is a rare disease and the end result of a destructive, inflammatory cholangiopathy, leading to fibrosis and biliary cirrhosis. It is classified into syndromic variety with various congenital anomalies and non-syndromic (isolated anomaly). We present here a 1-month-old female child with the syndromic variety of BA associated with polysplenia syndrome, dextrocardia, situs inversus totalis and malrotation of intestines. She developed jaundice in the first week of life. Kasai operation was performed but she developed cholangitis and septicemia 2.5 months after surgery and succumbed later.
Texto completo:
1
Colección:
01-internacional
Base de datos:
MEDLINE
Tipo de estudio:
Risk_factors_studies
Idioma:
En
Revista:
J Neonatal Surg
Año:
2014
Tipo del documento:
Article