Malignant triton tumor: Grand Round presentation of a rare aggressive case thoracolumbar spine tumor.
Eur Spine J
; 28(6): 1448-1452, 2019 06.
Article
en En
| MEDLINE
| ID: mdl-28924675
ABSTRACT
INTRODUCTION:
We report a rare and aggressive case of malignant triton tumor (MTT) at the thoracolumbar junction with foraminal extension mistreated as schwannoma. MATERIALS ANDMETHODS:
A 70-year-old man with a 2-year history of lower back pain and left L4 radiculopathy with no history of neurofibromatosis.RESULTS:
Pre-operative MRI suggested a typical schwannoma. Upon complete marginal resection, histological findings revealed a MTT. The patient presented with a local and regional recurrence and died 10 months after surgery. MTTs are a subgroup of malignant peripheral nerve sheath tumors, which develop from Schwann cells of peripheral nerves or within existing neurofibromas, and display rhabdomyoblastic differentiation.CONCLUSION:
Based on the Grand Round case and relevant literature, we present a case of a highly aggressive and fast-growing tumor with a very high local and distant recurrence. There is no consensus treatment plan available and patients usually die shortly after diagnosis.Palabras clave
Texto completo:
1
Colección:
01-internacional
Base de datos:
MEDLINE
Asunto principal:
Neoplasias de la Columna Vertebral
/
Neoplasias de la Vaina del Nervio
Tipo de estudio:
Diagnostic_studies
Límite:
Aged
/
Humans
/
Male
Idioma:
En
Revista:
Eur Spine J
Asunto de la revista:
ORTOPEDIA
Año:
2019
Tipo del documento:
Article
País de afiliación:
Francia