Severe Iron Metabolism Defects in Mice With Double Knockout of the Multicopper Ferroxidases Hephaestin and Ceruloplasmin.
Cell Mol Gastroenterol Hepatol
; 6(4): 405-427, 2018.
Article
en En
| MEDLINE
| ID: mdl-30182051
Palabras clave
CP, ceruloplasmin; Cp-/-, mice lacking CP in the whole body; DAB, 3,3'-diaminobenzidine; FDR, false discovery rate; FPN1, ferroportin 1; GI, gastrointestinal; HCI, hydrochloric acid; HEPH, hephaestin; Heph-/-, mice lacking HEPH in the whole body; Heph-/-Cp-/- or DKO, double-knockout mice lacking both HEPH and CP; Hephfl/fl, mice with floxed Heph alleles; Hephfl/flCp-/-, mice with floxed Heph alleles and lacking CP in the whole body; Hephint/int, mice lacking HEPH in the intestine alone; Hephint/intCp-/-, mice lacking HEPH in the intestine alone and lacking CP in the whole body; Hephsla/slaCp-/-, mice lacking CP in the whole body and expressing only the sla mutant form of HEPH; Intestinal Iron Absorption; Iron Deficiency Anemia; Iron Overload; MCF, multicopper ferroxidase; NTBI, non-transferrin bound iron; Non-Transferrin Bound Iron; PBS, phosphate-buffered saline; PCR, polymerase chain reaction; SD, standard deviation; TBST, Tris-buffered saline with 0.1% Tween-20; TF, transferrin; TIBC, total iron binding capacity; WT, wild-type; sla, sex-linked anemia
Texto completo:
1
Colección:
01-internacional
Base de datos:
MEDLINE
Asunto principal:
Ceruloplasmina
/
Hierro
/
Proteínas de la Membrana
Límite:
Animals
Idioma:
En
Revista:
Cell Mol Gastroenterol Hepatol
Año:
2018
Tipo del documento:
Article