Pulmonary mucoepidermoid carcinoma arising in a patient with Kartagener syndrome.
BMC Pulm Med
; 20(1): 93, 2020 Apr 16.
Article
en En
| MEDLINE
| ID: mdl-32299405
ABSTRACT
BACKGROUND:
Kartagener syndrome, an autosomal recessive disorder with a triad of chronic sinusitis, bronchiectasis, and situs inversus, is characterized by recurrent respiratory tract infections and chronic inflammation of the lung. Information on comorbidities other than infections in patients with Kartagener syndrome is currently limited. CASE PRESENTATION A 39-year-old, non-smoking female was diagnosed with Kartagener syndrome and admitted to Saitama Medical Center, Jichi Medical University, Japan. Computed tomography revealed an endobronchial massive shadow at the ostial site of the right upper lobe bronchus with atelectasis of the right upper lobe. The mass was surgically resected and pathologically diagnosed as mucoepidermoid carcinoma. The lesion had no vascular invasions and no metastases to the lungs or lymph nodes. The surgical margin was negative for carcinoma. Following surgery, the patient has been in good condition.CONCLUSIONS:
The present case showed different clinicopathological characteristics from those previously reported in cases of Kartagener syndrome complicated by carcinoma. To the best of our knowledge, this is the first reported case of a young, non-smoking female with comorbid Kartagener syndrome and pulmonary mucoepidermoid carcinoma. This case report may provide a new perspective on the complications of Kartagener syndrome.Palabras clave
Texto completo:
1
Colección:
01-internacional
Base de datos:
MEDLINE
Asunto principal:
Síndrome de Kartagener
/
Carcinoma Mucoepidermoide
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Neoplasias Pulmonares
Límite:
Adult
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Female
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Humans
Idioma:
En
Revista:
BMC Pulm Med
Año:
2020
Tipo del documento:
Article
País de afiliación:
Japón