Susac's syndrome: beneficial effects of corticosteroid therapy in a Japanese case.
Intern Med
; 40(2): 135-9, 2001 Feb.
Article
em En
| MEDLINE
| ID: mdl-11300147
ABSTRACT
Susac's syndrome is a rare disorder characterized by the triad of microangiopathy of the brain and retina with hearing loss. More than 50 affected individuals have been reported worldwide, all Caucasians. We herein identify the first Japanese patient with Susac's syndrome. A 36-year-old man developed recurrent subacute encephalopathy, bi- a lateral sensorineural hearing loss, and retinal arteriolar occlusions, caused by microangiopathy from a year previously. T2-weighted MRI showed multiple high-signal lesions ti predominantly in the periventricular white matter. During the exacerbated phase both high-dose intravenous methyl-prednisolone and oral prednisone therapy produced beneficial effects. He showed definite remission within 2 years from the disease onset.
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Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Metilprednisolona
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Prednisona
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Oclusão da Artéria Retiniana
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Papiledema
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Vasculite do Sistema Nervoso Central
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Perda Auditiva Bilateral
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Perda Auditiva Neurossensorial
/
Anti-Inflamatórios
Tipo de estudo:
Diagnostic_studies
/
Etiology_studies
/
Prognostic_studies
Limite:
Adult
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Humans
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Male
Idioma:
En
Revista:
Intern Med
Assunto da revista:
MEDICINA INTERNA
Ano de publicação:
2001
Tipo de documento:
Article