[Erdheim-Chester disease of the orbit with compressive optic neuropathy]. / Erdheim-Chester-Erkrankung der Orbita mit Kompressionsneuropathie.
Ophthalmologe
; 107(3): 266-9, 2010 Mar.
Article
em De
| MEDLINE
| ID: mdl-19777245
ABSTRACT
A 60-year-old man presented with left exophthalmos and deterioration in visual acuity of slow evolution. Bilateral orbital Erdheim-Chester disease was diagnosed. Systemic evaluation revealed a retroperitoneal fibrosis. Treatment with interferon-alpha followed, but bilateral compressive optic neuropathy with visual acuity deterioration and visual field defects evolved. Bilateral orbital decompression was performed.
Texto completo:
1
Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Doenças do Nervo Óptico
/
Doença de Erdheim-Chester
/
Síndromes de Compressão Nervosa
Tipo de estudo:
Diagnostic_studies
Limite:
Humans
/
Male
/
Middle aged
Idioma:
De
Revista:
Ophthalmologe
Assunto da revista:
OFTALMOLOGIA
Ano de publicação:
2010
Tipo de documento:
Article