Oral manifestations of autoimmune polyglandular syndrome type 1.
Spec Care Dentist
; 42(5): 531-535, 2022 Sep.
Article
em En
| MEDLINE
| ID: mdl-35182449
ABSTRACT
AIMS:
Autoimmune polyglandular syndrome type I (APS-I) is a rare condition of autosomal recessive and monogenic inheritance, which is characterized clinically by at least two signs of the classic triad mucocutaneous candidosis, hypoparathyroidism, and Addison's disease. This study aims to report the oral manifestations of APS-I in a 42-year-old woman, who attended the Special Care Dentistry Center. METHODS ANDRESULTS:
The patient presented with hypoparathyroidism, diabetes mellitus, and autoimmune hepatitis. Chronic hyperplastic candidosis (CHC) was the main oral manifestation and it was diagnosed based on clinical and cytologic characteristics. Microstomia, angular cheilitis, xerostomia, enamel hypoplasia, and microdontia were also present.CONCLUSIONS:
CHC was treated with topical nystatin and oral fluconazole, resulting in a significant improvement of the lesions.Palavras-chave
Texto completo:
1
Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Candidíase Mucocutânea Crônica
/
Doença de Addison
/
Poliendocrinopatias Autoimunes
/
Hipoplasia do Esmalte Dentário
/
Hipoparatireoidismo
Tipo de estudo:
Diagnostic_studies
Limite:
Adult
/
Female
/
Humans
Idioma:
En
Revista:
Spec Care Dentist
Ano de publicação:
2022
Tipo de documento:
Article
País de afiliação:
Brasil