Shrinking lung syndrome mimicking diaphragmatic palsy in systemic lupus erythematosus.
Pract Neurol
; 24(4): 313-315, 2024 Jul 16.
Article
em En
| MEDLINE
| ID: mdl-38423753
ABSTRACT
A 25-year-old woman presented with 1 year of progressive orthopnoea, initially explained as bilateral diaphragmatic paresis caused by seronegative myasthenia gravis. She required assisted ventilation and received pyridostigmine and corticosteroids. She had minimal (particularly proximal) symmetrical tetraparesis with apparent bilateral diaphragmatic weakness, but had normal sensation. Further investigation suggested an overlap myositis with shrinking lung syndrome from systemic lupus erythematosus. She improved following immunosuppression with pulse corticosteroids and rituximab, and at 3 months no longer needed bilevel positive airway pressure support.
Palavras-chave
Texto completo:
1
Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Paralisia Respiratória
/
Lúpus Eritematoso Sistêmico
Limite:
Adult
/
Female
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Humans
Idioma:
En
Revista:
Pract Neurol
/
Pract. neurol
/
Practical neurology
Ano de publicação:
2024
Tipo de documento:
Article
País de afiliação:
Índia