RESUMO
Incessant narrow QRS complex tachycardias may result in severe tachycardia-induced cardiomyopathy even if the heart rate during tachycardia is only moderately elevated. The risk of ventricular deterioration is particularly increased in patients with underlying congenital heart disease. In these patients, drug treatment is often insufficient. Thus, catheter ablation of the arrhythmogenic substrate is required in the majority of patients. After successful ablation, ventricular function may recover completely.
Assuntos
Cardiomiopatias , Ablação por Cateter , Cardiopatias Congênitas , Cardiomiopatias/diagnóstico , Cardiomiopatias/terapia , Eletrocardiografia , Humanos , Taquicardia/diagnóstico , Taquicardia/etiologiaAssuntos
Feixe Acessório Atrioventricular , Arritmias Cardíacas/cirurgia , Implante de Prótese Vascular/instrumentação , Prótese Vascular , Cateterismo Cardíaco , Ablação por Cateter , Técnica de Fontan , Cardiopatias Congênitas/cirurgia , Arritmias Cardíacas/etiologia , Arritmias Cardíacas/fisiopatologia , Eletrocardiografia , Técnicas Eletrofisiológicas Cardíacas , Humanos , Masculino , Politetrafluoretileno , Desenho de Prótese , Punções , Resultado do Tratamento , Adulto JovemRESUMO
A 2.5-year-old patient with complex congenital heart disease involving dextrocardia, atrioventricular and ventriculoarterial discordance, pulmonary stenosis, ventricular septal defect (VSD), atrial septal defect (ASD), and paroxysmal supraventricular tachycardia (SVT) underwent electrophysiological study. The tachycardia mechanism was diagnosed with cryomapping. The ability of cryomapping to have transient and reversible effect on the tissue, unlike radiofrequency (RF) ablation, helped in the establishment of diagnosis in this toddler with typical atrioventricular nodal reentrant tachycardia. Cryomapping can be an additional safe diagnostic utility in young patients with complex congenital heart disease.