Isolated Congenital Tracheobiliary Fistula.

BACKGROUND: Congenital tracheobiliary fistula is a rare developmental anomaly with a persistent communication between the biliary system and the trachea. CHARACTERISTICS: A 7-day-old baby with severe respiratory distress and aspiration pneumonia. OUTCOME: Tracheobilliary fistula identified on bronchoscopy. Open surgical excision of fistula was followed by improvement. MESSAGE: This condition should be considered in the differential diagnosis of intractable aspiration pneumonia.