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Transverse testicular ectopia is a rare anomaly characterized by testicular descent into the scrotum through the same inguinal canal. Here, we report the case of a 15-year-old boy diagnosed with transverse testicular ectopia wherein both testes descended through separate inguinal canals. He underwent a diagnostic laparoscopy which helped to identify both spermatic cords entering both inguinal canals separately. During scrotal exploration, both testes were found in the same side. Transseptal orchidopexy was performed. The short-term follow-up is uneventful.
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BACKGROUND: High level of androgens found in congenital adrenal hyperplasia (CAH) seems to have a deleterious effect on heart function. We therefore evaluate cardiac function of children with CAH in comparison with a healthy group. METHODS: We carried out a case-control study in the single endocrinology unit of the Mother and Child Center of Chantal Biya's Foundation. Cases were matched for age and genotypic sex to 2 healthy controls. We analyzed the ejection fraction (LVEF), fractional shortening and left ventricular mass; output and cardiac index; E and A waves velocities, E/A ratio and the mitral deceleration time and diameter of the left atrium; tricuspid annular plane systolic excursion and pulmonary artery systolic pressure were also measured. RESULTS: We included 19 patients with a median age of 6.26 ± 3.75 years and 38 controls stackable distribution. The left ventricular mass of cases was greater than that of controls. A case of reversible cardiomyopathy on hormone replacement therapy was found. For the cases, the average ejection fraction was 71.95 ± 7.88%; the average fractional shortening was 40.67 ± 7.02%. All these values ââwere higher than those of controls, although the difference was not statistically significant. Diastolic left ventricular function was more impaired among the cases. Right ventricular function was similar in both groups. These abnormalities were highly correlated to the late age at diagnosis and duration of treatment. CONCLUSION: This study shows an altered cardiac function in CAH compared to healthy control and highlights importance of an early diagnosis of cases, a tight control of androgens levels and a regular monitoring of cardiac function.
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Hiperplasia Suprarrenal Congênita/fisiopatologia , Coração/fisiopatologia , Adolescente , Camarões , Estudos de Casos e Controles , Criança , Pré-Escolar , Feminino , Testes de Função Cardíaca , Humanos , Lactente , MasculinoRESUMO
OBJECTIVE: The aim of this work was to describe the epidemiological, diagnostic and therapeutic aspects of undescended testicle in the of Pediatric Surgery service of the Yaoundé gyneco-obstetric and pediatric hospital. METHOD: Our study was retrospective, descriptive and analytical from June 2008 to December 2016; a period of 8 years and 6 months. Included in this study were records of pediatric patients aged 0 - 15 years who had been managed for an undescended testis in the Pediatric Surgery service of the Yaoundé gyneco-obstetric and pediatric hospital and followed up at our outpatient clinic. Data recorded included age, term of pregnancy at birth, time to presentation, presenting complaint, symptoms, location of the testis, surgical approach and procedure, complications and follow up. Open orchidopexy according to Surraco was the standard operation carried out for all our patients, a scrotal doppler ultrasound was systematic 30 days after the surgery and the child was scheduled for follow-up visits at 3, 6, 9 and 12 months postoperatively. RESULTS: Seventy-one patients were managed during the study period, giving a hospital frequency of 10 cases per annum. The average age of our patients was 5.8 years [1 day and 15 years]. The mean time to consultation was 4.5 years [1 day and 15 years]. Most patients consulted for absence of the testis (n = 62). All patients were full term births. Clinically, the undescended testis was categorized as: cryptorchidism (n = 45), ectopia testis (n = 2), intra-abdominal testis (n = 24), retractile testis (n = 7), vanishing testis (n = 4). The position of the undescended testis was: inguinal (n = 64), pelvic (n = 2) and abdominal (n = 5). Single stage open orchidopexy according to Surraco using an incision in the lower inguinal crease was performed in 66 cases (93%). Laparoscopy was used in 7% of cases for location of non-palpable testis. With a mean follow-up of 3 months, testicular atrophy was found in 5.6% of cases in our series.
BUT: Le but de ce travail était de décrire les aspects épidémiologiques, diagnostiques et thérapeutiques du testicule non descendu dans le Service de Chirurgie Pédiatrique de l'hôpital gynéco-obstétrique et pédiatrique de Yaoundé (HGOPY). PATIENTS ET MÉTHODE: Notre étude a été rétrospective et descriptive de Juin 2008 à Décembre 2016; soit une période de 8 ans et 6 mois dans le Service de Chirurgie Pédiatrique de l'hôpital gynéco-obstétrique et pédiatrique de Yaoundé. Ont été inclus dans cette étude, les dossiers des patients pédiatriques d'âge 10 15 ans ayant présenté un testicule non descendu pris en charge à HGOPY et revus en consultation.Les paramètres étudiés étaient: âge, terme, délai de consultation, motif de consultation, tableau clinique, topographie du testicule, voie d'abord, geste réalisé, morbidité, recul. L'abaissement testiculaire selon Surraco avait été de mise chez tous nos patients, une échographie doppler scrotale était systématique à J 30 post opératoire et l'enfant était revu en consultation de contrôle à 3 mois, 6 mois, 9 mois et 12 mois. RÉSULTATS: Soixante-onze patients ont été colligés et traités pendant la période d'étude, soit une fréquence annuelle de 10 cas. L'âge moyen de nos patients était de 5,8 ans [1 jour et 15 ans]. Le délai moyen de consultation était de 4,5 ans [1 jour et 15 ans]. L'absence de testicule était le principal motif de consultation (n=62). Tous les patients étaient nés à terme. Les tableaux cliniques étaient les suivant: testicule cryptorchide (n=45), testicule ectopique (n=2), testicule intra-abdominal (n=24), testicule oscillant (n=7), testicule évanescent ou « vanishing testis ¼ (n=4). La topographie du testicule non descendu a été: inguinale (n=64), pelvienne (n=2), abdominal (n=5). La voie d'abord a été inguinale dans un pli abdominal inférieur dans 66 cas (93%) et coelioscopique dans 7% des cas. Les gestes réalisés ont été dominés par l'abaissement testiculaire avec orchidopexie. Avec un recul moyen de 3 mois l'atrophie testiculaire a représenté 5,6% de notre série.
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UNLABELLED: Mixed gonadal dysgenesis is characterised by unilateral chromosomal abnormality, which is probably the result of anaphase lag during mitosis. The 45, XO/46, XY karyotype is the most common form of mosaicism involving the Y chromosome. It is a rare clinical entity with a worldwide incidence of 1.5/10,000 live births. Its epidemiology in Sub-Saharan Africa is not known. This study reports experience in the management of 3 cases at the Yaounde Gynecologic-Obstetric and Paediatric Hospital. From November 2009 to November 2014, 3 cases were successfully managed at our institution. RESULTS: All patients presented with asymmetrical gonadal differentiation. On one side of the body, a poorly-developed testicular gonad and on the other side a gonadal streak. A persistent MÏllerian remnant was equally found in the 3 cases. Management of mixed gonadal dysgenesis should be done in tertiary health care centres. A multidisciplinary team approach is recommended.
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Disgenesia Gonadal Mista/diagnóstico , Disgenesia Gonadal Mista/cirurgia , Adolescente , Camarões , Criança , Pré-Escolar , Humanos , MasculinoRESUMO
Syringocele or dilatation of the duct of the bulbo-urethral (Cowper's) gland is usually of congenital origin but can be acquired. It is a very rare deformity, <10 cases have been reported in literature. The main objective is to describe an additional case of syringocele of Cowper's glands and review the literature. An 18-month-old infant presented with a history of acute urinary retention 3 days after birth and a cystostomy was done. Voiding cystourethrogram was normal and cystourethroscopy showed a syringocele. Endoscopic incision was performed in our patient with satisfactory results. No complications were noted. Syringocele or cystic dilatation of Cowper's gland duct usually has a congenital aetiology. Diagnosis is confirmed by endoscopy. Treatment is by marsupialisation in the urethra by endoscopy. Syringocele is a rare pathology usually congenital. It should be suspected in all case of lower urinary tract obstruction in children.
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Glândulas Bulbouretrais/patologia , Doenças Uretrais/etiologia , Camarões , Humanos , Lactente , Masculino , Doenças Uretrais/diagnóstico , Doenças Uretrais/cirurgiaRESUMO
Introduction. Urethral strictures in boys denote narrowing of the urethra which can be congenital or acquired. In case of acquired strictures, the etiology is iatrogenic or traumatic and rarely infectious or inflammatory. The aim of this study was to highlight the diagnostic and therapeutic difficulties of acquired nontraumatic urethral strictures in boys in Yaoundé, Cameroon. Methodology. The authors report five cases of nontraumatic urethral strictures managed at the Pediatric Surgery Department of the YGOPH over a two-year period (November 2012-November 2014). In order to confirm the diagnosis of urethral stricture, all patients were assessed with both cystourethrography and urethrocystoscopy. Results. In all the cases the urethra was inflammatory with either a single or multiple strictures. The surgical management included internal urethrotomy (n = 1), urethral dilatation (n = 1), vesicostomy (n = 2), and urethral catheterization (n = 3). With a median follow-up of 8.2 months (4-16 months) all patients remained symptoms-free. Conclusion. The authors report the difficulties encountered in the diagnosis and management of nontraumatic urethral strictures in boys at a tertiary hospital in Yaoundé, Cameroon. The existence of an inflammatory etiology of urethral strictures in boys deserves to be considered.
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The sacrococcygeal teratoma is a rare congenital embryonal tumor with high potential for malignant transformation and therefore considered as a neonate surgical emergency. The authors report two cases of sacrococcygeal teratomas with late diagnosis and treatment. The first case was a degenerated sacrococcygeal teratoma revealed by paraplegia in a 17-month-old infant with multiple metastasis and fatal outcome. The second case was a 14-month-old infant with a benign infected form of sacrococcygeal teratoma, successfully treated surgically. The authors highlight the diagnostic difficulties still existing in the tropical environment, and recall the need for a prenatal diagnosis and early treatment.
Le tératome sacro-coccygien est une tumeur embryonnaire congénitale rare à fort potentiel de transformation maligne et donc considéré comme une urgence chirurgicale néonatale. Les auteurs rapportent deux cas de tératomes sacro coccygiens, de diagnostic et de prise en charge tardifs. Dans le premier cas, il s'agissait d'un tératome sacro-coccygien dégénéré révélé par une paraplégie chez un nourrisson de 17 mois avec de multiples localisations secondaires et une évolution fatale. Le deuxième cas concernait un nourrisson de 14 mois avec une forme bénigne surinfectée traitée chirurgicalement avec succès. Les auteurs mettent en relief les difficultés diagnostiques encore existant en milieu tropical, et rappellent la nécessité d'un diagnostic anténatal et d'une prise en charge précoce.
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INTRODUCTION: Pott's disease is a common entity in our hospital. The authors report their experience in the surgical treatment of Pott disease. PATIENTS AND METHODS: This is a retrospective study including all patients who underwent surgery for Pott's disease in our institution between November 1999 and November 2004. RESULTS: Forty-three patients were included, including 23 men and 20 women (ratio 1.15). Location of the disease was cervical (2 cases), dorsal (19 cases), dorsolumbar (2 cases) lumbar (16 cases) and sacrolumbar (4 cases). Ten patients were HIV positive (24%). The surgical indication was sometimes diagnostic, but predominantly therapeutic (medullary compression, instability or deformity). Spinal decompression alone was performed in 23 cases, associated with internal fixation of the spine (17 cases) or external immobilization (Halo Vest) in two cases. The anterior approach was used in four cases and a posterior approach in 38 cases. Decompression by posterior approach included 1 or 2 level laminectomy alone or associated with internal plate fixation (4 pedicle screws and 2 plates). There was no functional recovery in patients with a complete neurological deficit (Frankel A); those with a severe deficit (Frankel B) partially recovered, while those with more moderate deficits (Frankel C and D) recovered completely. Fusion was obtained (graft integration) regardless of the surgical approach used, progression of the deformity was stopped and early mobilization was possible. CONCLUSION: Surgery definitely plays a role in the diagnosis and treatment of Pott's disease, especially in countries where patients are seen at a late stage of the disease when complications have developed. Surgical decompression should not be delayed until lesions become ischemic and irreversible (Frankel A). LEVEL OF EVIDENCE: Level IV. Retrospective study.
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Placas Ósseas , Parafusos Ósseos , Vértebras Cervicais , Vértebras Lombares , Fusão Vertebral/métodos , Vértebras Torácicas , Tuberculose da Coluna Vertebral/cirurgia , Adolescente , Adulto , Idoso , Camarões , Criança , Feminino , Seguimentos , Humanos , Masculino , Pessoa de Meia-Idade , Radiografia , Estudos Retrospectivos , Resultado do Tratamento , Tuberculose da Coluna Vertebral/diagnóstico por imagem , Adulto JovemRESUMO
From July 2005 to November 2009, 38 neonates with surgical emergencies died in the neonatal unit of the Gyneco Obstetric and Pediatric Hospital Yaounde. The mortality rate of these emergencies was 43.1%, and those within the age group of 1 to 7 days were the most affected with a sex ratio of 1.2. The mean delay before consultation was 3.7 days. Half of the neonates had a birth weight of less than 2,500 g and 7 cases (18.4%) were premature. A medicalised ambulance was used for transfer to our unit in only half of the neonates. The main disorders were those affecting the digestive tract in 42.1% of our series. In 50% of our cases, there were associated malformations and 28 cases (73.7%) did not undergo surgery. Malnutrition and infection were the main complications in 60% of the cases. The authors discuss this deplorable situation and suggest recommendations for improvement.
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Mortalidade Hospitalar , Doenças do Recém-Nascido/mortalidade , Doenças do Recém-Nascido/cirurgia , Unidades de Terapia Intensiva Neonatal , Complicações na Gravidez/epidemiologia , Camarões/epidemiologia , Feminino , Ginecologia , Maternidades , Hospitais Pediátricos , Hospitais de Ensino , Humanos , Recém-Nascido , Doenças do Recém-Nascido/prevenção & controle , Gravidez , Complicações na Gravidez/prevenção & controle , Estudos Retrospectivos , Fatores de RiscoRESUMO
AIM: To improve the diagnosis of intussusceptions on infants and children in the African milieu. TOOLS AND METHOD: Within a period of 3 years, a retrospective study was carried out on 10 cases of intussusceptions noticed and treated in the paediatric surgical unit of GOPHY. RESULTS: We noticed a peak in frequency between the ages of 3 to 12 months with pre- dominance in the female gender 70% of cases. In average most cases consulted in a hospital 72 hours after the onset of symptoms. We however recorded delays between 24 hours and 7 days. 50% of parents saw treatment initiated on their children after a delay of 48 hours. All cases were treated surgically with good prognosis. The authors identify a delay in diagnoses in the African milieu and thus the treatment that follows. Literature is reviewed and solutions are proposed to improve the diagnosis of intussusceptions.