1.
ERJ Open Res
; 9(2)2023 Mar.
Artigo
em Inglês
| MEDLINE
| ID: mdl-36891069
RESUMO
Diffuse panniculitis is a rare manifestation of α1-ATD, albeit perhaps the most fulminant and life-threatening complication, associated usually with ZZ phenotype. Intravenous α1-AT treatment is lifesaving. https://bit.ly/3EDmCzT.