RESUMO
BACKGROUND: Sanjad--Sakati syndrome (SSS) is a genetic disease confined to Arab populations in the Middle- East countries and characterized by hypoparathyroidism, hypocalcaemia and hyperphosphataemia, severe intrauterine and postnatal growth failure, respiratory infection susceptibility prone, dwarfism, mental retardation, seizures, craniofacial dysmorphic features as retromicrognathia and abnormal dentition. CASE REPORT: A 12 year-old child was referred who needed dental treatment because of his oral and systemic condition. Radiographic findings showed agenesis of 12 permanent teeth (all canines and premolars). TREATMENT: Because of the child's physical limitations and cooperation, treatment was under general anaesthesia. Plaque removal, restorations and extractions of infected teeth were performed. FOLLOW-UP: The child was observed after one year, plaque removal was carried out and fluoride varnish was placed on all teeth. However, the patient died 18 months later as a result of pulmonary complications. CONCLUSION: People with poor systemic conditions and physical limitations are prone to dental health neglect. Early professional advice and treatment, and periodical follow-up can improve quality of life of these patients.