Acquired slow-channel syndrome.
Muscle Nerve
; 23(10): 1582-5, 2000 Oct.
Article
in En
| MEDLINE
| ID: mdl-11003795
ABSTRACT
We report the case of a 37-year-old man with clinical and electrophysiological features of hereditary slow-channel syndrome (SCS) and antibodies against acetylcholine receptors (AChR-Abs). He presented with weakness of shoulder and hand muscles. A supramaximal single stimulus to the motor nerves disclosed a double compound muscle action potential (CMAP). Repetitive stimulation of ulnar, suprascapular, and median nerves showed a CMAP decrement greater than 10%. The patient responded to pyridostigmine. This report confirms the importance of AChR-Ab titers in suspected cases of hereditary SCS because patients with positive AChR-Abs may have a better response to available treatments.
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Collection:
01-internacional
Database:
MEDLINE
Main subject:
Myasthenic Syndromes, Congenital
/
Muscles
Limits:
Adult
/
Humans
/
Male
Language:
En
Journal:
Muscle Nerve
Year:
2000
Document type:
Article