The rare coagulation disorders--review with guidelines for management from the United Kingdom Haemophilia Centre Doctors' Organisation.
Haemophilia
; 10(5): 593-628, 2004 Sep.
Article
in En
| MEDLINE
| ID: mdl-15357789
ABSTRACT
The rare coagulation disorders are heritable abnormalities of haemostasis that may present significant difficulties in diagnosis and management. This review summarizes the current literature for disorders of fibrinogen, and deficiencies of prothrombin, factor V, FV + VIII, FVII, FX, the combined vitamin K-dependent factors, FXI and FXIII. Based on both collective clinical experience and the literature, guidelines for management of bleeding complications are suggested with specific advice for surgery, spontaneous bleeding, management of pregnancy and the neonate. We have chosen to include a section on Ehlers-Danlos Syndrome because haematologists may be consulted about bleeding manifestations in such patients.
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Collection:
01-internacional
Database:
MEDLINE
Main subject:
Blood Coagulation Disorders
/
Practice Guidelines as Topic
Type of study:
Diagnostic_studies
/
Etiology_studies
/
Guideline
Limits:
Humans
Language:
En
Journal:
Haemophilia
Year:
2004
Document type:
Article