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Relief of CoA sequestration and restoration of mitochondrial function in a mouse model of propionic acidemia.
Subramanian, Chitra; Frank, Matthew W; Tangallapally, Rajendra; Yun, Mi-Kyung; White, Stephen W; Lee, Richard E; Rock, Charles O; Jackowski, Suzanne.
Affiliation
  • Subramanian C; Department of Infectious Diseases, St. Jude Children's Research Hospital, Memphis, Tennessee, United States.
  • Frank MW; Department of Infectious Diseases, St. Jude Children's Research Hospital, Memphis, Tennessee, United States.
  • Tangallapally R; Department of Chemical Biology and Therapeutics, St. Jude Children's Research Hospital, Memphis, Tennessee, United States.
  • Yun MK; Department of Structural Biology, St. Jude Children's Research Hospital, Memphis, Tennessee, United States.
  • White SW; Department of Structural Biology, St. Jude Children's Research Hospital, Memphis, Tennessee, United States.
  • Lee RE; St. Jude Graduate School of Biomedical Sciences, St. Jude Children's Research Hospital, Memphis, Tennessee, United States.
  • Rock CO; Department of Microbiology, Immunology and Biochemistry, University of Tennessee Health Science Center, Memphis, Tennessee, United States.
  • Jackowski S; Department of Chemical Biology and Therapeutics, St. Jude Children's Research Hospital, Memphis, Tennessee, United States.
J Inherit Metab Dis ; 46(1): 28-42, 2023 01.
Article in En | MEDLINE | ID: mdl-36251252

Full text: 1 Collection: 01-internacional Database: MEDLINE Main subject: Propionic Acidemia Limits: Animals Language: En Journal: J Inherit Metab Dis Year: 2023 Document type: Article

Full text: 1 Collection: 01-internacional Database: MEDLINE Main subject: Propionic Acidemia Limits: Animals Language: En Journal: J Inherit Metab Dis Year: 2023 Document type: Article