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Genetic ablation of Saposin-D in Krabbe disease eliminates psychosine accumulation but does not significantly improve demyelination.
Watanabe, Takashi; Tsuboi, Kazuhito; Matsuda, Nobuaki; Ishizuka, Yuta; Go, Shinji; Watanabe, Etsuko; Ono, Ayaka; Okamoto, Yasuo; Matsuda, Junko.
Affiliation
  • Watanabe T; Department of Pathophysiology and Metabolism, Kawasaki Medical School, Okayama, Japan.
  • Tsuboi K; Department of Pharmacology, Kawasaki Medical School, Okayama, Japan.
  • Matsuda N; Central Research Institute, Kawasaki Medical School, Okayama, Japan.
  • Ishizuka Y; Department of Pathophysiology and Metabolism, Kawasaki Medical School, Okayama, Japan.
  • Go S; Department of Pathophysiology and Metabolism, Kawasaki Medical School, Okayama, Japan.
  • Watanabe E; Department of Pathophysiology and Metabolism, Kawasaki Medical School, Okayama, Japan.
  • Ono A; Department of Pathophysiology and Metabolism, Kawasaki Medical School, Okayama, Japan.
  • Okamoto Y; Department of Pharmacology, Kawasaki Medical School, Okayama, Japan.
  • Matsuda J; Department of Pathophysiology and Metabolism, Kawasaki Medical School, Okayama, Japan.
J Neurochem ; 166(4): 720-746, 2023 08.
Article in En | MEDLINE | ID: mdl-37337846

Full text: 1 Collection: 01-internacional Database: MEDLINE Main subject: Leukodystrophy, Globoid Cell Type of study: Prognostic_studies Limits: Animals Language: En Journal: J Neurochem Year: 2023 Document type: Article

Full text: 1 Collection: 01-internacional Database: MEDLINE Main subject: Leukodystrophy, Globoid Cell Type of study: Prognostic_studies Limits: Animals Language: En Journal: J Neurochem Year: 2023 Document type: Article