Florid cemento-osseous dysplasia and peripheral giant cell granuloma in a patient with neurofibromatosis 1
An. bras. dermatol
; 92(2): 249-252, Mar.-Apr. 2017. graf
Article
em En
| LILACS
| ID: biblio-838046
Biblioteca responsável:
BR1.1
ABSTRACT
Abstract We report a 35-year-old mulatto female patient with neurofibromatosis Type 1 who presented with facial asymmetry. The patient had two lesions florid cemento-osseous dysplasia associated with peripheral giant cell granuloma. She was referred for surgical treatment of the peripheral giant cell granuloma and the florid cemento-osseous dysplasia was treated conservatively by a multidisciplinary team. So far, no changes have been observed in the patient's clinical status. We observed no recurrence of peripheral giant cell granuloma. To the best of our knowledge, the present case is the first report of a patient with neurofibromatosis Type 1 associated with a giant cell lesion and florid cemento-osseous dysplasia.
Palavras-chave
Texto completo:
1
Coleções:
01-internacional
Base de dados:
LILACS
Assunto principal:
Osteomielite
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Granuloma de Células Gigantes
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Neurofibromatose 1
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Assimetria Facial
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Displasia Fibrosa Óssea
Limite:
Adult
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Female
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Humans
Idioma:
En
Revista:
An. bras. dermatol
Ano de publicação:
2017
Tipo de documento:
Article