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Isolated pulmonary hypertension in diffuse cutaneous systemic sclerosis successfully treated with long-term plasma exchange.
Ferri, C; Emdin, M; Storino, F A; Giuggioli, D; Longombardo, G; Greco, F; Fertig, N; Medsger, T A.
Afiliação
  • Ferri C; Department of Internal Medicine, University of Pisa, Italy. c.ferri@int.med.unipi.it
Scand J Rheumatol ; 29(3): 198-200, 2000.
Article em En | MEDLINE | ID: mdl-10898077
ABSTRACT
Isolated pulmonary hypertension (PHT) in patients with diffuse cutaneous systemic sclerosis (dSSc) is one of the most severe complication. Here we report the case of a 22 year-old white woman with anti-U3RNP antibody-positive dSSc complicated by severe, isolated PHT successfully treated with long-term plasma exchange. This beneficial effect persisted for two years, even after plasma exchange discontinuation. This is the first observation of isolated PHT in dSSc responsive to plasma exchange therapy.
Assuntos
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Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Troca Plasmática / Escleroderma Sistêmico / Hipertensão Pulmonar Tipo de estudo: Etiology_studies Limite: Adult / Female / Humans Idioma: En Revista: Scand J Rheumatol Ano de publicação: 2000 Tipo de documento: Article
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Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Troca Plasmática / Escleroderma Sistêmico / Hipertensão Pulmonar Tipo de estudo: Etiology_studies Limite: Adult / Female / Humans Idioma: En Revista: Scand J Rheumatol Ano de publicação: 2000 Tipo de documento: Article