Bilateral congenital diaphragmatic hernia with absent pleura and pericardium.
Birth Defects Res A Clin Mol Teratol
; 73(9): 624-7, 2005 Sep.
Article
em En
| MEDLINE
| ID: mdl-16001446
ABSTRACT
BACKGROUND:
Bilateral congenital diaphragmatic hernia is a rare form of diaphragmatic hernia. Independently, pericardial defects are an extremely rare phenomenon. In the case presented, we provide the first complete description of an infant with bilateral congenital diaphragmatic hernia with complete agenesis of the pericardium and inferior parietal pleura. CASE A male infant was born at 38 weeks of gestation with a prenatal diagnosis of left-sided congenital diaphragmatic hernia. After 1 week of aggressive management, the patient was taken to the operating room for repair. Intraoperatively, the patient was found to have absence of the diaphragm bilaterally, no pleura inferiorly, and no pericardium. A biological mesh was used to construct a diaphragm. At 6 months of age, the patient is growing normally, requiring only supplemental oxygen without pressure support.CONCLUSIONS:
Embryologically, this anomaly represents complete lack of development of the pleurocardial folds, pleuroperitoneal folds, and transverse septum, which is previously unreported.
Buscar no Google
Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Pericárdio
/
Pleura
/
Anormalidades Múltiplas
/
Hérnias Diafragmáticas Congênitas
/
Hérnia Diafragmática
Tipo de estudo:
Diagnostic_studies
/
Observational_studies
/
Prognostic_studies
Limite:
Female
/
Humans
/
Male
/
Newborn
/
Pregnancy
Idioma:
En
Revista:
Birth Defects Res A Clin Mol Teratol
Ano de publicação:
2005
Tipo de documento:
Article