Chronic myositis with cardiomyopathy and respiratory failure associated with mild form of organ-specific autoimmune diseases.
Clin Rheumatol
; 26(11): 1917-9, 2007 Nov.
Article
em En
| MEDLINE
| ID: mdl-17674117
ABSTRACT
We report the four patients with chronic myositis characterized by a very slow progression with cardiomyopathy and frequently with marked respiratory muscle weakness associated with other organ-specific autoimmune diseases such as primary biliary cirrhosis. The histopathology of the muscle showed many degenerative and regenerative fibers, but inflammatory-cell infiltration were minimal. The patients showed favorable response to high-dose corticosteroid treatment. Because of these clinical features, these patients are sometimes misdiagnosed as muscular dystrophy and not treated properly. It is important to distinguish this type of treatable myositis.
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Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Insuficiência Respiratória
/
Doenças Autoimunes
/
Cardiomiopatias
/
Miosite
Tipo de estudo:
Diagnostic_studies
/
Risk_factors_studies
Limite:
Adult
/
Aged
/
Female
/
Humans
/
Middle aged
Idioma:
En
Revista:
Clin Rheumatol
Ano de publicação:
2007
Tipo de documento:
Article