Surgical treatment of valvular and supravalvular aortic stenosis in homozygous familial hypercholesterolemia.
Gen Thorac Cardiovasc Surg
; 64(2): 98-100, 2016 Feb.
Article
em En
| MEDLINE
| ID: mdl-24505024
A 61-year-old male with homozygous familial hypercholesterolemia presented with dyspnea and syncope. He had been treated with low-density lipoprotein apheresis for 26 years. Echocardiography and computed tomography showed severe valvular and supravalvular aortic stenosis. Computed tomography and cardiac catheterization revealed a severely calcified narrowed aortic root and an occlusion in the proximal right coronary artery. During surgery, the ascending aorta was replaced under deep hypothermic circulatory arrest without aortic cross-clamping. After that, the aortic root from the annulus to the sino-tubular junction was enlarged with a two-ply bovine pericardial patch. An aortic valve replacement with a 17 mm mechanical valve and coronary artery bypass grafting to the right coronary artery were performed. The patient recovered from the surgery without any cerebrovascular complications.
Palavras-chave
Texto completo:
1
Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Retalhos Cirúrgicos
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Implante de Prótese de Valva Cardíaca
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Estenose Aórtica Supravalvular
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Hiperlipoproteinemia Tipo II
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Lipoproteínas LDL
Tipo de estudo:
Diagnostic_studies
Limite:
Animals
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Humans
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Male
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Middle aged
Idioma:
En
Revista:
Gen Thorac Cardiovasc Surg
Ano de publicação:
2016
Tipo de documento:
Article