Perivascular fibrosis and IgG4-related disease: a case report.
Reumatismo
; 66(3): 245-8, 2014 Nov 06.
Article
em En
| MEDLINE
| ID: mdl-25376960
ABSTRACT
Immunoglobulin G4-related disease (IgG4-RD) is a newly recognized fibroinflammatory condition which can potentially involve any organ. Some characteristic histopathologic features with lymphoplasmacytic infiltrate, an increased number of IgG4+ cells, storiform fibrosis and obliterative phlebitis are the mainstay for diagnosis. Serum IgG4 levels often increase. We report the case of a patient with perivascular fibrotic lesions involving the aortic arch and the splenic hilum, with a surgical biopsy-proven diagnosis of IgG4-related disease. The patient is now undergoing a low-dose corticosteroid maintenance therapy without evidence of new localizations of the disease. This case highlights the need for increasing awareness and recognition of this new, emerging clinical condition.
Texto completo:
1
Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Fibrose Retroperitoneal
/
Imunoglobulina G
Limite:
Female
/
Humans
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Middle aged
Idioma:
En
Revista:
Reumatismo
Ano de publicação:
2014
Tipo de documento:
Article