Perioperative management of a child with glutaric aciduria type I undergoing cardiac surgery.
A A Case Rep
; 1(1): 5-7, 2013 Oct.
Article
em En
| MEDLINE
| ID: mdl-25611601
ABSTRACT
Patients with glutaric aciduria type I are at risk for acute striatal injury precipitated by catabolic stress. Here, we report the successful interdisciplinary anesthetic and perioperative management of a child with glutaric aciduria type I undergoing cardiac surgery with extracorporeal circulation. Given the central focus on prevention of acute striatal injury, our anesthetic strategy emphasized avoiding a high protein load, high-dose inotropics, especially epinephrine (associated with impaired glucose utilization), deliberate hyperventilation, and other interventions associated with systemic inflammatory response.
Texto completo:
1
Coleções:
01-internacional
Base de dados:
MEDLINE
Idioma:
En
Revista:
A A Case Rep
Ano de publicação:
2013
Tipo de documento:
Article