Hepatic Angiosarcoma with Dyskeratosis Congenita.
Intern Med
; 54(22): 2867-72, 2015.
Article
em En
| MEDLINE
| ID: mdl-26568000
ABSTRACT
Nail dystrophy, oral leukoplakia and abnormal skin pigmentation are the defining features of dyskeratosis congenita. Dyskeratosis congenita is a disorder of poor telomere maintenance and is known to increase the risk of developing multiple types of malignancy. However, there are few reports of liver tumors arising in dyskeratosis congenita patients. We herein report the second case of hepatic angiosarcoma arising from dyskeratosis congenita a 23-year-old man was introduced to our hospital due to the detection of multiple tumors in the liver. A histological analysis showed angiosarcoma that stained positive for antibodies to both CD31 and blood coagulation factor VIII.
Texto completo:
1
Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Leucoplasia Oral
/
Disceratose Congênita
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Hemangiossarcoma
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Neoplasias Hepáticas
Limite:
Adult
/
Humans
/
Male
Idioma:
En
Revista:
Intern Med
Ano de publicação:
2015
Tipo de documento:
Article