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Osteoblast Malfunction Caused by Cell Stress Response to Procollagen Misfolding in α2(I)-G610C Mouse Model of Osteogenesis Imperfecta.
Mirigian, Lynn S; Makareeva, Elena; Mertz, Edward L; Omari, Shakib; Roberts-Pilgrim, Anna M; Oestreich, Arin K; Phillips, Charlotte L; Leikin, Sergey.
Afiliação
  • Mirigian LS; Section on Physical Biochemistry, Eunice Kennedy Shriver National Institute of Child Health and Human Development (NICHD), National Institutes of Health, Bethesda, MD 20892.
  • Makareeva E; Department of Cell Biology, University of Texas Medical Branch, Galveston, TX 77555.
  • Mertz EL; Section on Physical Biochemistry, Eunice Kennedy Shriver National Institute of Child Health and Human Development (NICHD), National Institutes of Health, Bethesda, MD 20892.
  • Omari S; Section on Physical Biochemistry, Eunice Kennedy Shriver National Institute of Child Health and Human Development (NICHD), National Institutes of Health, Bethesda, MD 20892.
  • Roberts-Pilgrim AM; Section on Physical Biochemistry, Eunice Kennedy Shriver National Institute of Child Health and Human Development (NICHD), National Institutes of Health, Bethesda, MD 20892.
  • Oestreich AK; Section on Physical Biochemistry, Eunice Kennedy Shriver National Institute of Child Health and Human Development (NICHD), National Institutes of Health, Bethesda, MD 20892.
  • Phillips CL; Division of Biological Sciences, University of Missouri, Columbia, MO 65211.
  • Leikin S; Department of Biochemistry, University of Missouri, Columbia, MO 65211.
J Bone Miner Res ; 31(8): 1608-1616, 2016 08.
Article em En | MEDLINE | ID: mdl-26925839

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Osteoblastos / Osteogênese Imperfeita / Estresse Fisiológico / Pró-Colágeno / Dobramento de Proteína / Colágeno Tipo I / Mutação Limite: Animals Idioma: En Revista: J Bone Miner Res Ano de publicação: 2016 Tipo de documento: Article

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Osteoblastos / Osteogênese Imperfeita / Estresse Fisiológico / Pró-Colágeno / Dobramento de Proteína / Colágeno Tipo I / Mutação Limite: Animals Idioma: En Revista: J Bone Miner Res Ano de publicação: 2016 Tipo de documento: Article