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Mounier-Kuhn syndrome: a case of tracheal smooth muscle remodeling.
Cook, Daniel P; Adam, Ryan J; Abou Alaiwa, Mahmoud H; Eberlein, Michael; Klesney-Tait, Julia A; Parekh, Kalpaj R; Meyerholz, David K; Stoltz, David A.
Afiliação
  • Cook DP; Department of Internal Medicine University of Iowa Iowa City Iowa USA; Department of Molecular Physiology and Biophysics University of Iowa Iowa City Iowa USA.
  • Adam RJ; Department of Internal Medicine University of Iowa Iowa City Iowa USA; Department of Biomedical Engineering University of Iowa Iowa City Iowa USA.
  • Abou Alaiwa MH; Department of Internal Medicine University of Iowa Iowa City Iowa USA.
  • Eberlein M; Department of Internal Medicine University of Iowa Iowa City Iowa USA.
  • Klesney-Tait JA; Department of Internal Medicine University of Iowa Iowa City Iowa USA.
  • Parekh KR; Department of Cardiothoracic Surgery University of Iowa Iowa City Iowa USA.
  • Meyerholz DK; Department of Pathology University of Iowa Iowa City Iowa USA.
  • Stoltz DA; Department of Internal Medicine University of Iowa Iowa City Iowa USA; Department of Molecular Physiology and Biophysics University of Iowa Iowa City Iowa USA; Department of Biomedical Engineering University of Iowa Iowa City Iowa USA; Pappajohn Biomedical Institute University of Iowa Iowa City Iowa
Clin Case Rep ; 5(2): 93-96, 2017 02.
Article em En | MEDLINE | ID: mdl-28174630
ABSTRACT
Mounier-Kuhn syndrome is a rare clinical disorder characterized by tracheobronchial dilation and recurrent lower respiratory tract infections. While the etiology of the disease remains unknown, histopathological analysis of Mounier-Kuhn airways demonstrates that the disease is, in part, characterized by cellular changes in airway smooth muscle.
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Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Idioma: En Revista: Clin Case Rep Ano de publicação: 2017 Tipo de documento: Article

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Idioma: En Revista: Clin Case Rep Ano de publicação: 2017 Tipo de documento: Article