Cutaneous Malignant Peripheral Nerve Sheath Tumor.
Surg Pathol Clin
; 10(2): 337-343, 2017 Jun.
Article
em En
| MEDLINE
| ID: mdl-28477884
ABSTRACT
Cutaneous malignant peripheral nerve sheath tumors (MPNSTs) are rare sarcomas of neuroectodermal origin arising in the dermis and/or subcutis. In contrast with their deep soft tissue and visceral counterparts, cutaneous MPNSTs are rarely associated with neurofibromatosis type 1. Two main subtypes of cutaneous MPNST can be distinguished histologically conventional (ie, spindle cell) and epithelioid MPNST. The 2 subtypes also differ in predilection for deep versus superficial locations, association with preexistent benign peripheral nerve sheath tumors and S100 immunohistochemistry. Herein, we review current knowledge of cutaneous MPNST and discuss its differential diagnosis.
Palavras-chave
Texto completo:
1
Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Neoplasias do Sistema Nervoso Periférico
/
Neoplasias Cutâneas
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Neurilemoma
Limite:
Humans
/
Male
Idioma:
En
Revista:
Surg Pathol Clin
Ano de publicação:
2017
Tipo de documento:
Article