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NEDD4-family E3 ligase dysfunction due to PKHD1/Pkhd1 defects suggests a mechanistic model for ARPKD pathobiology.
Kaimori, Jun-Ya; Lin, Cheng-Chao; Outeda, Patricia; Garcia-Gonzalez, Miguel A; Menezes, Luis F; Hartung, Erum A; Li, Ao; Wu, Guanqing; Fujita, Hideaki; Sato, Yasunori; Nakanuma, Yasuni; Yamamoto, Satoko; Ichimaru, Naotsugu; Takahara, Shiro; Isaka, Yoshitaka; Watnick, Terry; Onuchic, Luiz F; Guay-Woodford, Lisa M; Germino, Gregory G.
Afiliação
  • Kaimori JY; Department of Nephrology, Osaka University Graduate School of Medicine, 2-2 Yamadaoka, Suita, Osaka, 565-0871, Japan. kaimori@att.med.osaka-u.ac.jp.
  • Lin CC; Department of Advanced Technology of Transplantation, Osaka University Graduate School of Medicine, 2-2 Yamadaoka, Suita, Osaka, 565-0871, Japan. kaimori@att.med.osaka-u.ac.jp.
  • Outeda P; National Institute of Diabetes and Digestive and Kidney Diseases, National Institutes of Health, Bldg 31, 9A52, 31 Center Drive, Bethesda, MD20892, USA.
  • Garcia-Gonzalez MA; University of Maryland School of Medicine, Division of Nephrology, 22S Green St, Baltimore, MD21201, USA.
  • Menezes LF; Laboratorio de Investigacion en Nefroloxia, Complexo Hospitalario Universitario de Santiago, Travesía de Choupana, s/n 15706, Santiago de Compostela, Spain.
  • Hartung EA; National Institute of Diabetes and Digestive and Kidney Diseases, National Institutes of Health, Bldg 31, 9A52, 31 Center Drive, Bethesda, MD20892, USA.
  • Li A; Division of Nephrology, Children's Hospital of Philadelphia, Perelman School of the University of Pennsylvania, 3401 Civic Center Boulevard, CTRB 9207, Philadelphia, PA, 19104, USA.
  • Wu G; Center of Translational Cancer Research and Therapy, State Key Laboratory of Molecular Oncology, Cancer Hospital and Institute, Chinese Academy of Medical Sciences and Peking Union Medical College, Beijing, 100021, China.
  • Fujita H; Center of Translational Cancer Research and Therapy, State Key Laboratory of Molecular Oncology, Cancer Hospital and Institute, Chinese Academy of Medical Sciences and Peking Union Medical College, Beijing, 100021, China.
  • Sato Y; Graduate School of Pharmaceutical Science, Nagasaki International University, 2825-7 Huis Ten Bosch-Cho, Sasebo, Nagasaki, 859-3298, Japan.
  • Nakanuma Y; Departments of Human Pathology, Kanazawa University Graduate School of Medicine, 13-1 Takara-cho, Kanazawa, 920-8640, Japan.
  • Yamamoto S; Department of Pathology, Shizuoka Cancer Center, 1007 Shimonagakubo, Nagaizumi-cho, Sunto-gun, Shizuoka, 411-8777, Japan.
  • Ichimaru N; Department of Nephrology, Osaka University Graduate School of Medicine, 2-2 Yamadaoka, Suita, Osaka, 565-0871, Japan.
  • Takahara S; Department of Advanced Technology of Transplantation, Osaka University Graduate School of Medicine, 2-2 Yamadaoka, Suita, Osaka, 565-0871, Japan.
  • Isaka Y; Department of Advanced Technology of Transplantation, Osaka University Graduate School of Medicine, 2-2 Yamadaoka, Suita, Osaka, 565-0871, Japan.
  • Watnick T; Department of Nephrology, Osaka University Graduate School of Medicine, 2-2 Yamadaoka, Suita, Osaka, 565-0871, Japan.
  • Onuchic LF; University of Maryland School of Medicine, Division of Nephrology, 22S Green St, Baltimore, MD21201, USA.
  • Guay-Woodford LM; Department of Medicine, Division of Nephrology, University of Sao Paulo, Dr. Arnald Ave, 455-Cerqueira Cesar, Sao Paulo, CEP01246903-903, Brazil.
  • Germino GG; Children's National Health System, 6th Floor Main Hospital, Center 6, 111 Michigan Ave NW, Washington, DC, 20010, USA.
Sci Rep ; 7(1): 7733, 2017 08 10.
Article em En | MEDLINE | ID: mdl-28798345
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Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Rim Policístico Autossômico Recessivo / Receptores de Superfície Celular / Ubiquitina-Proteína Ligases Nedd4 Limite: Animals / Humans / Male Idioma: En Revista: Sci Rep Ano de publicação: 2017 Tipo de documento: Article
Texto completo
Imprimir
XML
PubMed Links
Buscar no Google

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Rim Policístico Autossômico Recessivo / Receptores de Superfície Celular / Ubiquitina-Proteína Ligases Nedd4 Limite: Animals / Humans / Male Idioma: En Revista: Sci Rep Ano de publicação: 2017 Tipo de documento: Article