Treatment of Hepatic Embryonal Undifferentiated Sarcoma With Cardiothoracic Involvement.
World J Pediatr Congenit Heart Surg
; 11(4): NP199-NP202, 2020 Jul.
Article
em En
| MEDLINE
| ID: mdl-30319025
Thorough study is required to decide the appropriate management of hepatic tumors in children. We present a case report of a hepatic embryonal undifferentiated sarcoma with unfavorable prognosis in a nine-year-old girl. After undergoing a detailed cancer characteristics and extension study, a two-stage surgery approach was decided. The hepatic tumor resection was the first procedure to be performed. One week later, under cardiopulmonary bypass, deep hypothermia, and circulatory arrest, thrombectomy of the inferior vena cava and right atrium was accomplished, plus thromboendarterectomy of the right pulmonary artery. During a four-year follow-up, the patient continues to be disease-free.
Palavras-chave
Texto completo:
1
Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Sarcoma
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Ponte Cardiopulmonar
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Neoplasias Cardíacas
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Procedimentos Cirúrgicos Cardíacos
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Neoplasias Hepáticas
Tipo de estudo:
Diagnostic_studies
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Prognostic_studies
Limite:
Child
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Female
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Humans
Idioma:
En
Revista:
World J Pediatr Congenit Heart Surg
Ano de publicação:
2020
Tipo de documento:
Article